Advertisement

Less Common Forms of Vasculitis

  • Eric L. Matteson
  • John H. Stone

Abstract

The hallmark of Cogan's syndrome is the presence of ocular inflammation and audiovestibular dysfunction. These findings may be accompanied by the evidence of a systemic vasculitis that involves large blood vessels. Interstitial keratitis is the most common form of ocular involvement. Audiovestibular dysfunction may lead to the acute onset of vertigo, tinnitus, nausea, and vomiting. Vasculitis in Cogan's syndrome may take the form of aortitis, renal artery stenosis, or occlusion of the great vessels.

Keywords

Systemic Lupus Erythematosus Chronic Urticaria Ocular Inflammation Leukocytoclastic Vasculitis Urticarial Vasculitis 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

References

  1. Davis MD, Brewer JD. Urticarial vasculitis and hypocomplementemic urticarial vasculitis syndrome. Immunol Allergy Clin North Am 2004;24:183PubMedCrossRefGoogle Scholar
  2. Davis MDP, Daoud MS, Kirby B, et al Clinicopathologic correlation of hypocomplementemic and normocomplementemic urticarial vascu-litis. J Am Acad Dermatol 1998;38:899PubMedCrossRefGoogle Scholar
  3. Gibson LE, El-Azhary RA. Erythema elevatum diutinum. Clin Dermatol 2000;18:295–99PubMedCrossRefGoogle Scholar
  4. Gluth MB, Baratz KH, Matteson EL, et al Cogan's syndrome: a retrospective review of 60 patients throughout a half-century. Mayo Clin Proc 2006;81:483–8PubMedCrossRefGoogle Scholar
  5. Grasland A, Pouchot P, Hachulla E, et al Typical and atypical Cogan's syndrome: 32 cases and review of the literature. Rheumatology 2004;43:1007–15PubMedCrossRefGoogle Scholar
  6. Mazlumzadeh M, Matteson EL. Cogan's syndrome: an audiovestibular, ocular, and systemic autoimmune disease. Rheum Dis Clin North Am 2007;33:855–74PubMedCrossRefGoogle Scholar
  7. Mehregan DR, Hall MJ, Gibson LE. Urticarial vasculitis: a histopatho-logic and clinical review of 72 cases. J Am Acad Dermatol 1992;26(3 Pt 2):441–8PubMedCrossRefGoogle Scholar
  8. Pafanisi, Pafanisi E, Vincenti V, et al Cochlear implantation and Cogan's syndrome. Otol Neurotol 2003;24:601–4CrossRefGoogle Scholar
  9. Riente L, Taglione E, Berrettini S. Efficacy of methotrexate in Cogan's syndrome. J Rheumatol 1996;23:1830–1PubMedGoogle Scholar
  10. Sunderkötter C, Bonsmann G, Sindrilaru A, et al Management of leuko-cytoclasticvasculitis. J Dermatol Treat 2005;16:193–206CrossRefGoogle Scholar
  11. Toppe E, Haas N, Henz BM. Neutrophilic urticaria: clinical features, histologic changes, and possible mechanisms. Br J Dermatol 1998;138:248–53PubMedCrossRefGoogle Scholar
  12. Vollertsen R, McDonald T, Younge B, et al Cogan's syndrome: 18 cases and a review of the literature. Mayo Clin Proc 1986;61: 344–61PubMedCrossRefGoogle Scholar
  13. Wahl CE, Bouldin MB, Gibson LE. Erythema elevatum diutinum: clinical, histopathologic, and immunohistochemical characteristics of six patients. Am J Dermatopathol 2005;27:397–400PubMedCrossRefGoogle Scholar
  14. Wisnieski JJ, Baer AN, Christensen J, et al Hypocomplementemic urti-carial vasculitis syndrome: clinical and serologic findings in 18 patients. Medicine 1995;74:24–41PubMedCrossRefGoogle Scholar

Copyright information

© Springer Science+Business Media B.V. 2009

Authors and Affiliations

  • Eric L. Matteson
    • 2
  • John H. Stone
    • 1
  1. 1.Clinical RheumatologyMassachusetts General HospitalBoston
  2. 2.Mayo ClinicDivision of RheumatologyRochesterUSA

Personalised recommendations