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Perivascular Tumors

  • Steven D. BillingsEmail author
  • Rajiv M. Patel
Chapter

Abstract

This chapter focuses on a group of tumors that arise from perivascular “myoid” modified smooth muscle cells that invest blood vessels. This family of tumors includes angioleiomyoma, glomus tumor, glomuvenous malformation (glomangioma), glomangiomyoma, myopericytoma, myofibroma, glomus tumor of uncertain malignant potential, and malignant glomus tumor. This group of tumors, consisting of round to spindled cells that invest a proliferation of bland blood vessels, shows significant histologic and immunophenotypic overlap. Indeed, perivascular myoid cell tumors are often hybrid lesions that demonstrate a combination of histopathologic features of the aforementioned entities.

Keywords

Angioleiomyoma Glomus tumor Glomuvenous malformation (glomangioma) Glomangiomyoma Myopericytoma Myofibroma Glomus tumor of uncertain malignant potential and malignant glomus tumor 

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Copyright information

© Springer Science+Business Media, LLC, part of Springer Nature 2019

Authors and Affiliations

  1. 1.Department of PathologyCleveland ClinicClevelandUSA
  2. 2.Department of PathologyUniversity of Michigan Medical SchoolAnn ArborUSA

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