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Pediatric Case of Sickle Cell Disease

  • Melissa GerstleEmail author
  • Katherine Baum
  • Charles T. Quinn
  • Dean W. BeebeEmail author
Chapter

Abstract

Sickle Cell: Children with sickle cell disease (SCD) often have cognitive, behavioral, and mood-related difficulties, in part due to the effect of their medical condition on the central nervous system. They are at high risk for neurological injury and insult, with as many as one-third having neurological complications. This chapter details a pediatric case of SCD, assessed through repeated neuropsychological evaluations. It highlights the unique challenges of assessing a “moving target”—the interaction between a protean chronic illness and the developing brain.

Keywords

Sickle cell disease Pediatric Cognitive Neuropsychology Medical/neurological assessment 

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Copyright information

© Springer Science+Business Media, LLC, part of Springer Nature 2019

Authors and Affiliations

  1. 1.Division of Behavioral Medicine and Clinical Psychology, Cincinnati Children’s Hospital Medical Center, Department of PediatricsUniversity of Cincinnati College of MedicineCincinnatiUSA
  2. 2.Division of Hematology, Cincinnati Children’s Hospital Medical Center, Department of PediatricsUniversity of Cincinnati College of MedicineCincinnatiUSA

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