Metabolic Changes Following Splenic Transplantation in a Case of Gaucher’s Disease

  • Carl G. Groth
  • Rolf Blomstrand
  • Lars Hagenfeldt
  • Per-Arne Ockerman
  • Karin Samuelsson
  • Lars Svennerholm
Part of the Advances in Experimental Medicine and Biology book series (AEMB, volume 19)

Abstract

The fact that the highest activity of glucocerebrosidase is normally found in the spleen (2) has suggested the possibility of splenic transplantation as a means of enzyme replacement in Gaucher’s disease (1). Technically successful splenic homotransplantations have been reported by Starzl and co-workers in six patients with diseases other than lipidosis (3, 9).

Keywords

Ceramide Level Phenyl Phosphate Skeletal Pain Royal Veterinary College Produce Cell Death 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer Science+Business Media New York 1972

Authors and Affiliations

  • Carl G. Groth
    • 1
  • Rolf Blomstrand
    • 1
  • Lars Hagenfeldt
    • 1
  • Per-Arne Ockerman
    • 1
  • Karin Samuelsson
    • 1
  • Lars Svennerholm
    • 1
  1. 1.Karolinska Institute and Royal Veterinary CollegeUniversity of Gothenburg and University of LundStockholmSweden

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