Deficiency of Specific Proteins in the Inborn Errors of Mucopolysaccharide Metabolism

  • Elizabeth F. Neufeld
  • Robert W. Barton
  • Michael Cantz
  • Jeffery G. Derge
  • Clara W. Hall
  • Hans Kresse
  • James F. Scott
Part of the Advances in Experimental Medicine and Biology book series (AEMB, volume 19)

Abstract

This paper will summarize recent studies on the nature and function of those proteins which are deficient in the mucopolysaccharidoses.

Keywords

Heparan Sulfate Inborn Error Dermatan Sulfate Hunter Syndrome Metachromatic Leukodystrophy 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer Science+Business Media New York 1972

Authors and Affiliations

  • Elizabeth F. Neufeld
    • 1
  • Robert W. Barton
    • 1
  • Michael Cantz
    • 1
  • Jeffery G. Derge
    • 1
  • Clara W. Hall
    • 1
  • Hans Kresse
    • 1
  • James F. Scott
    • 1
  1. 1.National Institute of Arthritis and Metabolic DiseasesNational Institutes of HealthBethesdaUSA

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