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Congenital Mitral Stenosis

  • Azin AlizadeaslEmail author
  • Anita Sadeghpour
Chapter

Abstract

Congenital mitral stenosis (MS) refers to the parachute deformity of the valve. In this condition, condensed chordae tendineae join and attach into a single large papillary muscle, usually with thickened leaflets of the mitral valve (MV), fusion of the chordae tendineae, accessory MV tissue, and supravalvular ring of the connective tissue rising at the base of the atrial aspect of the MV leaflets. Associated cardiac lesions are common and consist of coarctation of the aorta, patent ductus arteriosus, left ventricular outflow tract obstruction, and persistent left superior vena cava [1].

Keywords

Congenital Mitral Stenosis Parachute deformity Supra valvular ring Mitral valve regurgitation Balloon valvuluplasty 

Supplementary material

Video 40.1

Transthoracic echocardiography in short axis view showing divided mitralorifice into two components (DOMV) (AVI 9086 kb)

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Copyright information

© Springer-Verlag London 2014

Authors and Affiliations

  1. 1.Echocardiography Lab, Department of CardiologyRajaie Cardiovascular Medical and Research Center, Iran University of Medical ScienceTehranIran
  2. 2.Echocardiography Lab, Department of CardiologyAdult Congenital Heart Disease Clinic, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical ScienceTehranIran

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