Dilated, Restrictive/Infiltrative, and Hypertrophic Cardiomyopathies

  • Rory B. Weiner
  • Aaron L. Baggish
  • Aaron L. Baggish


Cardiomyopathies represent a heterogeneous group of heart muscle diseases that are a major cause of morbidity and mortality. Classification schemes for cardiomyopathy have been complex, and efforts have been made to classify the disease states based on myocardial characteristics and etiologies. The etiology, diagnosis, and management of dilated cardiomyopathy (DCM), restrictive/infiltrative cardiomyopathy, and hypertrophic cardiomyopathy (HCM) are the subject of this chapter and several features of each form of cardiomyopathy are highlighted in Table 17-1.


Sudden Cardiac Death Implantable Cardioverter Defibrillator Arrhythmogenic Right Ventricular Cardiomyopathy Constrictive Pericarditis Cardiac Amyloidosis 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.



Angiotensin converting enzyme


Atrial fibrillation


Anti-nuclear antibody


Aortic regurgitation


Angiotensin receptor blocker


Arrhythmogenic right ventricular cardiomyopathy


B-type natriuretic peptide


Coronary artery disease




Cardiac resynchronization therapy


Computed tomography


Chest x-ray


Dilated cardiomyopathy


Early peak diastolic tissue velocity




Hypertrophic cardiomyopathy


Human immunodeficiency virus


Hypertrophic obstructive cardiomyopathy


Implantable cardioverter defibrillator


Left ventricle or left ventricular


Left ventricular ejection fraction


Left ventricular hypertrophy


Left ventricular outflow tract


Mitral regurgitation


Magnetic resonance imaging


N-terminal pro B-type natriuretic peptide


Right ventricle or right ventricular


Systolic anterior motion


Sudden cardiac death


Serum protein electrophoresis

Supplementary material

Video 17-1

DCM (AVI 14959 kb)

Video 17-2

Amyloid (AVI 17528 kb)

Video 17-3

HCM (AVI 9632 kb)


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Copyright information

© Springer-Verlag London 2014

Authors and Affiliations

  • Rory B. Weiner
    • 1
  • Aaron L. Baggish
    • 2
  • Aaron L. Baggish
    • 3
  1. 1.Harvard Medical School Cardiovascular Performance Program, Cardiology Division, Department of MedicineMassachusetts General HospitalBostonUSA
  2. 2.Harvard Medical SchoolBostonUSA
  3. 3.Cardiovascular Performance Program, Cardiology Division, Department of MedicineMassachusetts General HospitalBostonUSA

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