Anomalies of the Systemic and Pulmonary Arteries

  • Arno A. W. RoestEmail author
  • Lucia J. M. Kroft
  • Lars Grosse-Wortmann
Part of the Medical Radiology book series (MEDRAD)


Congenital abnormalities of the thoracic systemic and pulmonary arteries can occur in isolation or in the setting of a complex cardiovascular malformation. Severe or complex vascular defects are usually diagnosed and corrected in childhood. Infrequently, anomalies of the systemic and pulmonary arteries present during adulthood. After correction of a cardiovascular malformation most children survive into adulthood. In adults, the most common indication for imaging is to evaluate post-treatment sequelae. Understanding the underlying pathology and possible complications that may occur during follow-up is essential for planning imaging studies. Furthermore, knowledge on the different imaging modalities, including their strengths and limitations for assessing anomalies of the systemic and pulmonary arteries, is important.

Supplementary material

Movie 1

14-Year old male patient with recurrent pulmonary infection. CT angiography showing complete vascular ring: double aortic arch with large right arch and small left arch with an atretic segment (fibrous strand) in connection to the descending aorta. The movie highlights the symmetrical branching of the arch vessels and the small left arch with an atretic segment. See Fig. 11 for the vessel anatomy (AVI 123654 kb)


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Copyright information

© Springer International Publishing AG 2018

Authors and Affiliations

  • Arno A. W. Roest
    • 1
    Email author
  • Lucia J. M. Kroft
    • 2
  • Lars Grosse-Wortmann
    • 3
  1. 1.Department of Paediatrics, Willem Alexander Children’s HospitalLeiden University Medical CenterLeidenThe Netherlands
  2. 2.Section Head of Cardiothoracic Radiology, Department of RadiologyLeiden University Medical CenterLeidenThe Netherlands
  3. 3.Section Head, Cardiovascular Magnetic Resonance, The Hospital for Sick ChildrenUniversity of TorontoTorontoCanada

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