Skip to main content

Atrial Isomerism

  • Chapter
  • First Online:
  • 2435 Accesses

Abstract

This chapter includes morphology, clinical manifestations, diagnosis, natural and unnatural course, treatment, including Kawashima operation and Fontan operation, and fetal diagnosis of congenital heart disease typically associated with right and left (atrial) isomerism. Positional abnormalities of the heart and anomalies of noncardiac organs typically seen in atrial isomerism are also presented.

This is a preview of subscription content, log in via an institution.

Buying options

Chapter
USD   29.95
Price excludes VAT (USA)
  • Available as PDF
  • Read on any device
  • Instant download
  • Own it forever
eBook
USD   189.00
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Softcover Book
USD   249.99
Price excludes VAT (USA)
  • Compact, lightweight edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info
Hardcover Book
USD   329.99
Price excludes VAT (USA)
  • Durable hardcover edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Purchases are for personal use only

Learn about institutional subscriptions

Suggested Reading

  1. Bae EJ, Lee JY, Noh CI, Kim WH, Kim YJ. Sinus node dysfunction after Fontan modifications-influence of surgical method. Int J Cardiol. 2003;88:285–91.

    Article  Google Scholar 

  2. Bartz PJ, Driscoll DJ, Dearani JA, et al. Early and late results of the modified Fontan operation for Heterotaxy syndrome 30 years of experience in 142 patients. J Am Coll Cardiol. 2006;48:2301–5.

    Article  Google Scholar 

  3. Brown JW, Ruzmetov M, Vijay P, et al. Pulmonary arteriovenous malformations in children after the Kawashima operation. Ann Thorac Surg. 2005;80:1592–6.

    Article  Google Scholar 

  4. Choi M, Borenstein SH, Hornberger L, Langer JC. Heterotaxia syndrome: The role of screening for intestinal rotation abnormalities. Arch Dis Child. 2005;90:813–5.

    Article  CAS  Google Scholar 

  5. Hsu JY, Wang JK, Lin MT, et al. Clinical implications of major aortopulmonary collateral arteries in patients with right isomerism. Ann Thorac Surg. 2006;82:153–7.

    Article  Google Scholar 

  6. Kawashima Y, Kitamura S, Matsuda H, et al. Total cavopulmonary shunt operation in complex cardiac anomalies. A new operation. J Thorac Cardiovasc Surg. 1984;87:74–81.

    CAS  PubMed  Google Scholar 

  7. Kim SJ, Kim WH, Lim HG, Lee CH, Lee JY. Improving results of the Fontan procedure in patients with heterotaxy syndrome. Ann Thorac Surg. 2006;82:1245–51.

    Article  Google Scholar 

  8. Lee MY, Won HS, Shim JY, Lee PR, et al. Prenatal diagnosis of atrial isomerism in the Korean population. Obstet Gynecol Sci. 2014;57:193–200.

    Article  Google Scholar 

  9. Mahle WT, Silverman NH, Marx GR, Anderson RH. Echo-morphological correlates concerning the functionally univentricular heart in the setting of isomeric atrial appendages. Cardiol Young. 2006;16:35–42.

    Article  Google Scholar 

  10. Morales DL, Braud BE, Booth JH, et al. Heterotaxy patients with total anomalous pulmonary venous return: Improving surgical results. Ann Thorac Surg. 2006;82:1621–8.

    Article  Google Scholar 

  11. Nagel BH, Williams H, Stewart L, et al. Splenic state in surviving patients with visceral heterotaxy. Cardiol Young. 2005;15:469–73.

    Article  Google Scholar 

  12. Park IS, Kim YH, Ko JK. Bilateral patent ductus arteriosus and nonconfluent pulmonary arteries in neonates as shown by radial artery angiography. Tex Heart Inst J. 1997;24:384–5.

    CAS  PubMed  PubMed Central  Google Scholar 

  13. Phoon CK, Neil CA. Asplenia syndrome: Insight into embryology through an analysis of cardiac and extracardiac anomalies. Am J Cardiol. 1994;73:581–7.

    Article  CAS  Google Scholar 

  14. Smith A, Ho SY, Anderson RH, et al. The diverse cardiac morphology seen in hearts with isomerism of the atrial appendages with reference to the disposition of the specialised conduction system. Cardiol Young. 2006;16:437–54.

    Article  Google Scholar 

  15. Steinberg J, Alfieris GM, Brandt B 3rd, et al. New approach to the surgical management of pulmonary arteriovenous malformations after cavopulmonary anastomosis. Ann Thorac Surg. 2003;75:1640–2.

    Article  Google Scholar 

  16. Tchervenkov CI, Jacobs ML, Del Duca D. Surgery for the functionally univentricular heart in patients with visceral heterotaxy. Cardiol Young. 2006;16:72–9.

    Article  Google Scholar 

  17. Yun TJ, Al-Radi OO, Adatia I, Caldarone CA, et al. Contemporary management of right atrial isomerism: effect of evolving therapeutic strategies. J Thorac Cardiovasc Surg. 2006;131:1108–13.

    Article  Google Scholar 

Download references

Author information

Authors and Affiliations

Authors

Editor information

Editors and Affiliations

Rights and permissions

Reprints and permissions

Copyright information

© 2019 Springer Nature Singapore Pte Ltd.

About this chapter

Check for updates. Verify currency and authenticity via CrossMark

Cite this chapter

Park, I.S., Goo, H.W. (2019). Atrial Isomerism. In: Park, I. (eds) An Illustrated Guide to Congenital Heart Disease. Springer, Singapore. https://doi.org/10.1007/978-981-13-6978-0_25

Download citation

  • DOI: https://doi.org/10.1007/978-981-13-6978-0_25

  • Published:

  • Publisher Name: Springer, Singapore

  • Print ISBN: 978-981-13-6977-3

  • Online ISBN: 978-981-13-6978-0

  • eBook Packages: MedicineMedicine (R0)

Publish with us

Policies and ethics