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Megacystis Microcolon Intestinal Hypoperistalsis Syndrome: MMIHS

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Hirschsprung’s Disease and the Allied Disorders

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Abstract

Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS) is a rare congenital condition, and such patients tend to present with abdominal distension, a largely dilated nonobstructive bladder, microcolon, and severe functional intestinal obstruction without structural atresia or stenosis in the neonatal period. Currently, the etiology is not well understood, and there is no specific treatment for this condition. The majority of MMIHS patients repeat the intestinal obstruction and enteritis, so they require long-term PN and drainage stomas. The prognosis remains poor.

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Authors and Affiliations

  1. Department of Pediatric Surgery, Osaka Women’s and Children’s Hospital, Izumi, Osaka, Japan

    Hideki Soh

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  1. Hideki Soh
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Correspondence to Hideki Soh .

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Editors and Affiliations

  1. Department of Pediatric Surgery, Kyushu University, Fukuoka, Fukuoka, Japan

    Tomoaki Taguchi

  2. Department of Pediatric Surgery, St. Luke’s International Hospital, Chuo-Ku, Tokyo, Japan

    Hiroshi Matsufuji

  3. Department of Pediatric Surgery, Kagoshima University, Kagoshima, Kagoshima, Japan

    Satoshi Ieiri

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Soh, H. (2019). Megacystis Microcolon Intestinal Hypoperistalsis Syndrome: MMIHS. In: Taguchi, T., Matsufuji, H., Ieiri, S. (eds) Hirschsprung’s Disease and the Allied Disorders. Springer, Singapore. https://doi.org/10.1007/978-981-13-3606-5_40

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  • DOI: https://doi.org/10.1007/978-981-13-3606-5_40

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  • Publisher Name: Springer, Singapore

  • Print ISBN: 978-981-13-3605-8

  • Online ISBN: 978-981-13-3606-5

  • eBook Packages: MedicineMedicine (R0)

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