Abstract
Total colonic aganglionosis (TCA) is a rare form of Hirschsprung disease and is defined as aganglionosis extending to the cecum or distal ileum. The mortality rate of this disease declined dramatically recently, but the morbidity rate is still high. Although several operative procedures have been adopted for TCA such as Martin, Duhamel, Soave, Swenson, and colon patch, with some modifications, the optimal procedure is not apparent, and we need to develop a novel treatment strategy to improve the high morbidity rate after pull-through operation.
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Kanamori, Y. (2019). Surgical Management of Total Colonic Aganglionosis and Extensive Aganglionosis. In: Taguchi, T., Matsufuji, H., Ieiri, S. (eds) Hirschsprung’s Disease and the Allied Disorders. Springer, Singapore. https://doi.org/10.1007/978-981-13-3606-5_25
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