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Surgical Management of Aortic Pathology pp 553–559Cite as

Morphology of the Ascending Aorta in Bicuspid Aortic Valve Disease

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Abstract

The spectrum of bicuspid aortic valve (BAV) disease encompasses not only maldevelopment of the aortic valve but also abnormalities of the thoracic aorta, including aortic root and ascending aortic dilatation. Insidious formation of thoracic aortic aneurysm (TAA) can lead to aortic dissection or rupture with necropsy series suggesting a 5–10 times higher risk of aortic dissection in BAV compared to patients with a trileaflet aortic valve.

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Author information

Authors and Affiliations

  1. Department of Clinical Genetics, Addenbrooke’s Hospital, Cambridge, UK

    Matina Prapa

  2. Adult Congenital Heart Centre and Centre for Pulmonary Hypertension, Royal Brompton Hospital, and The National Heart and Lung Institute, Imperial College, London, UK

    M. A. Gatzoulis

Authors
  1. Matina Prapa
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  2. M. A. Gatzoulis
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Corresponding author

Correspondence to Matina Prapa .

Editor information

Editors and Affiliations

  1. Fmr Royal Brompton Hospital, London, UK

    Olaf H. Stanger

  2. Royal Brompton Hospital, London, UK

    John R. Pepper

  3. Heart and Vascular Institute, Cleveland Clinic, Cleveland, OH, USA

    Lars G. Svensson

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Prapa, M., Gatzoulis, M.A. (2019). Morphology of the Ascending Aorta in Bicuspid Aortic Valve Disease. In: Stanger, O., Pepper, J., Svensson, L. (eds) Surgical Management of Aortic Pathology. Springer, Vienna. https://doi.org/10.1007/978-3-7091-4874-7_37

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  • DOI: https://doi.org/10.1007/978-3-7091-4874-7_37

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  • Online ISBN: 978-3-7091-4874-7

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