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The Cardiomyopathies

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Abstract

The cardiomyopathies are a heterogeneous group of disease of the myocardium. Historically in the WHO/International Society and Federation of Cardiology classification of 1996, cardiomyopathies were defined as primary disorders of unknown cause. Heart muscle diseases of known cause or associated with systemic disorders were classified as secondary. However, this distinction between primary and secondary heart muscle disease has become redundant, as the cause of previously idiopathic disorders has been discovered. Recently different classifications have been proposed to identify the different types of cardiomyopathies. There is no ideal classification; however, from an echocardiographic point of view, the classification based on structure and function is the most useful. This chapter will describe hypertrophic cardiomyopathy, dilated cardiomyopathy, restrictive cardiomyopathy, arrhythmogenic right ventricular cardiomyopathy, and left ventricular noncompaction according to the ESC classification.

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Correspondence to Ferdinando Luca Lorini .

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Lorini, F.L., Rizza, A., Ferri, F. (2019). The Cardiomyopathies. In: Sarti, A., Lorini, F. (eds) Textbook of Echocardiography for Intensivists and Emergency Physicians. Springer, Cham. https://doi.org/10.1007/978-3-319-99891-6_14

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  • DOI: https://doi.org/10.1007/978-3-319-99891-6_14

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-99890-9

  • Online ISBN: 978-3-319-99891-6

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