Skip to main content

Overview of the Intensive Care of the Adult with Congenital Heart Disease

  • Chapter
  • First Online:
Book cover Intensive Care of the Adult with Congenital Heart Disease

Part of the book series: Congenital Heart Disease in Adolescents and Adults ((CHDAA))

  • 886 Accesses

Abstract

There are now more adults than children living with congenital heart disease, many of whom have moderately to severely complex defects. As a group, these patients are hospitalized more than the general population, and many require intensive care. Adults with congenital heart disease are a highly variable group of patients, many of whom have antecedent chronic medical problems that may complicate or be complicated by critical illness, such as congestive hepatopathy and hepatic disease, renal impairment, arrhythmia, coagulopathy, and thrombosis. The intensive care team, whether in a children’s or adult hospital, needs to be prepared to handle this growing population of patients.

This is a preview of subscription content, log in via an institution to check access.

Access this chapter

Chapter
USD 29.95
Price excludes VAT (USA)
  • Available as PDF
  • Read on any device
  • Instant download
  • Own it forever
eBook
USD 149.00
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Hardcover Book
USD 199.99
Price excludes VAT (USA)
  • Durable hardcover edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Purchases are for personal use only

Institutional subscriptions

References

  1. Warnes CA, Liberthson R, Danielson GK, Dore A, Harris L, Hoffman JI, et al. Task force 1: the changing profile of congenital heart disease in adult life. J Am Coll Cardiol. 2001;37(5):1170–5.

    Article  CAS  Google Scholar 

  2. Marelli AJ, Mackie AS, Ionescu-Ittu R, Rahme E, Pilote L. Congenital heart disease in the general population: changing prevalence and age distribution. Circulation. 2007;115(2):163–72.

    Article  Google Scholar 

  3. Mackie AS, Pilote L, Ionescu-Ittu R, Rahme E, Marelli AJ. Health care resource utilization in adults with congenital heart disease. Am J Cardiol. 2007;99(6):839–43.

    Article  Google Scholar 

  4. Verheugt CL, Uiterwaal CS, van der Velde ET, Meijboom FJ, Pieper PG, Sieswerda GT, et al. The emerging burden of hospital admissions of adults with congenital heart disease. Heart. 2010;96(11):872–8.

    Article  Google Scholar 

  5. Kaemmerer H, Bauer U, Pensl U, Oechslin E, Gravenhorst V, Franke A, et al. Management of emergencies in adults with congenital cardiac disease. Am J Cardiol. 2008;101(4):521–5.

    Article  Google Scholar 

  6. Opotowsky AR, Siddiqi OK, Webb GD. Trends in hospitalizations for adults with congenital heart disease in the U.S. J Am Coll Cardiol. 2009;54(5):460–7.

    Article  Google Scholar 

  7. Blalock A. The technique of creation of an artificial ductus arteriosus in the treatment of pulmonic stenosis. J Thorac Surg. 1947;16(3):244–57.

    CAS  PubMed  Google Scholar 

  8. Pierce WS, Waldhausen JA, Berman W Jr, Whitman V. Late results of the subclavian flap procedure in infants with coarctation of the thoracic aorta. Circulation. 1978;58(3 Pt 2):I78–82.

    CAS  PubMed  Google Scholar 

  9. Wang A, Book WM, McConnell M, Lyle T, Rodby K, Mahle WT. Prevalence of hepatitis C infection in adult patients who underwent congenital heart surgery prior to screening in 1992. Am J Cardiol. 2007;100(8):1307–9.

    Article  Google Scholar 

  10. Asrani SK, Asrani NS, Freese DK, Phillips SD, Warnes CA, Heimbach J, et al. Congenital heart disease and the liver. Hepatology. 2012;56:1160.

    Article  Google Scholar 

  11. Shteyer E, Yatsiv I, Sharkia M, Milgarter E, Granot E. Serum transaminases as a prognostic factor in children post cardiac surgery. Pediatr Int. 2011;53(5):725–8.

    Article  CAS  Google Scholar 

  12. Dimopoulos K, Diller GP, Koltsida E, Pijuan-Domenech A, Papadopoulou SA, Babu-Narayan SV, et al. Prevalence, predictors, and prognostic value of renal dysfunction in adults with congenital heart disease. Circulation. 2008;117(18):2320–8.

    Article  Google Scholar 

  13. Somerville J. Management of adults with congenital heart disease: an increasing problem. Annu Rev Med. 1997;48:283–93.

    Article  CAS  Google Scholar 

  14. Khairy P, Aboulhosn J, Gurvitz MZ, Opotowsky AR, Mongeon FP, Kay J, et al. Arrhythmia burden in adults with surgically repaired tetralogy of Fallot: a multi-institutional study. Circulation. 2010;122(9):868–75.

    Article  Google Scholar 

  15. Zipes DP, Camm AJ, Borggrefe M, Buxton AE, Chaitman B, Fromer M, et al. ACC/AHA/ESC 2006 guidelines for management of patients with ventricular arrhythmias and the prevention of sudden cardiac death—executive summary: a report of the American College of Cardiology/American Heart Association Task Force and the European Society of Cardiology Committee for Practice Guidelines (Writing Committee to Develop Guidelines for Management of Patients with Ventricular Arrhythmias and the Prevention of Sudden Cardiac Death) Developed in collaboration with the European Heart Rhythm Association and the Heart Rhythm Society. Eur Heart J. 2006;27(17):2099–140.

    Article  Google Scholar 

  16. Lam W, Friedman RA. Electrophysiology issues in adult congenital heart disease. Methodist Debakey Cardiovasc J. 2011;7(2):13–7.

    Article  Google Scholar 

  17. Geva T. Repaired tetralogy of Fallot: the roles of cardiovascular magnetic resonance in evaluating pathophysiology and for pulmonary valve replacement decision support. J Cardiovasc Magn Reson. 2011;13:9.

    Article  Google Scholar 

  18. Backer CL. 12th annual C. Walton Lillehei memorial lecture in cardiovascular surgery: Fontan conversion—the Chicago experience. Cardiol Young. 2011;21(Suppl 2):169–76.

    Article  Google Scholar 

  19. Diller GP, Giardini A, Dimopoulos K, Gargiulo G, Muller J, Derrick G, et al. Predictors of morbidity and mortality in contemporary Fontan patients: results from a multicenter study including cardiopulmonary exercise testing in 321 patients. Eur Heart J. 2010;31(24):3073–83.

    Article  Google Scholar 

  20. Odegard KC, McGowan FX Jr, Zurakowski D, DiNardo JA, Castro RA, del Nido PJ, et al. Coagulation factor abnormalities in patients with single-ventricle physiology immediately prior to the Fontan procedure. Ann Thorac Surg. 2002;73(6):1770–7.

    Article  Google Scholar 

  21. Odegard KC, McGowan FX Jr, Zurakowski D, Dinardo JA, Castro RA, del Nido PJ, et al. Procoagulant and anticoagulant factor abnormalities following the Fontan procedure: increased factor VIII may predispose to thrombosis. J Thorac Cardiovasc Surg. 2003;125(6):1260–7.

    Article  Google Scholar 

  22. Jensen AS, Johansson PI, Bochsen L, Idorn L, Sorensen KE, Thilen U, et al. Fibrinogen function is impaired in whole blood from patients with cyanotic congenital heart disease. Int J Cardiol. 2013;167(5):2210–4.

    Article  CAS  Google Scholar 

  23. Sandoval J, Santos LE, Cordova J, Pulido T, Gutierrez G, Bautista E, et al. Does anticoagulation in Eisenmenger syndrome impact long-term survival? Congenit Heart Dis. 2012;7(3):268–76.

    Article  Google Scholar 

  24. Valente AM, Bhatt AB, Cook S, Earing MG, Gersony DR, Aboulhosn J, et al. The CALF (congenital heart disease in adults lower extremity systemic venous health in Fontan patients) study. J Am Coll Cardiol. 2010;56(2):144–50.

    Article  Google Scholar 

  25. Dimopoulos K, Diller GP, Giannakoulas G, Petraco R, Chamaidi A, Karaoli E, et al. Anemia in adults with congenital heart disease relates to adverse outcome. J Am Coll Cardiol. 2009;54(22):2093–100.

    Article  Google Scholar 

Download references

Author information

Authors and Affiliations

Authors

Corresponding author

Correspondence to Jeremy Nicolarsen .

Editor information

Editors and Affiliations

Rights and permissions

Reprints and permissions

Copyright information

© 2019 Springer International Publishing AG, part of Springer Nature

About this chapter

Check for updates. Verify currency and authenticity via CrossMark

Cite this chapter

Nicolarsen, J., Kay, J. (2019). Overview of the Intensive Care of the Adult with Congenital Heart Disease. In: da Cruz, E., Macrae, D., Webb, G. (eds) Intensive Care of the Adult with Congenital Heart Disease. Congenital Heart Disease in Adolescents and Adults. Springer, Cham. https://doi.org/10.1007/978-3-319-94171-4_2

Download citation

  • DOI: https://doi.org/10.1007/978-3-319-94171-4_2

  • Published:

  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-94170-7

  • Online ISBN: 978-3-319-94171-4

  • eBook Packages: MedicineMedicine (R0)

Publish with us

Policies and ethics