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Congenital Disorders of the Skull Base

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Abstract

Chiari malformation, basilar impression and Rathke’s cleft cysts are congenital disorders at the skull base that can become of therapeutical relevance if clinical symptoms occur. Surgery is the only treatment option in all cases. The indication for treatment is mainly focused on clinical complaints and the consecutive effect on the patient’s quality of life. CT and MR imaging findings determine the kind of surgical procedure.

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References

  1. Chiari H. Über Veränderungen des Kleinhirns infolge von Hydrocephalie des Grosshirns. Dtsch Med Wochenschr. 1891;17:1172–5.

    Article  Google Scholar 

  2. Guo SL, Zhou DB, Yu XG, Yin YH, Qiao GY. Posterior C1-C2 screw and rod instrument for reduction and fixation of basilar invagination with atlantoaxial dislocation. Eur Spine J. 2014;23(8):1666–72.

    Article  Google Scholar 

  3. Klekamp J. Treatment of basilar invagination. Eur Spine J. 2014;23(8):1656–65.

    Article  Google Scholar 

  4. Lang J. Skull base and related structures. Atlas of clinical anatomy. Stuttgart/New York: Schattauer; 2001. p. 22–3.

    Google Scholar 

  5. Larkin S, Karavitaki N, Ansorge O. Rathke’s cleft cyst. Handb Clin Neurol. 2014;124:255–69.

    Article  Google Scholar 

  6. Menezes AH. Craniovertebral junction abnormalities. In: Albright AL, Pollack IF, Adelson PD, editors. Principles and practice of pediatric neurosurgery. New York/Stuttgart: Thieme; 2008.

    Google Scholar 

  7. Soleau S, Tubbs RS, Oakes WJ. Chiari malformations. In: Albright AL, Pollack IF, Adelson PD, editors. Principles and practice of pediatric neurosurgery. New York/Stuttgart: Thieme; 2008.

    Google Scholar 

  8. Xia H, Yin Q, Ai F, Ma X, Wang J, Wu Z, Zhang K, Liu J, Xu J. Treatment of basilar invagination with atlantoaxial dislocation: atlantoaxial joint distraction and fixation with transoral atlantoaxial reduction plate (TARP) without odontoidectomy. Eur Spine J. 2014;23(8):1648–55.

    Article  Google Scholar 

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Correspondence to Alexander König .

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König, A. (2018). Congenital Disorders of the Skull Base. In: König, A., Spetzger, U. (eds) Surgery of the Skull Base. Springer, Cham. https://doi.org/10.1007/978-3-319-64018-1_7

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  • DOI: https://doi.org/10.1007/978-3-319-64018-1_7

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-64017-4

  • Online ISBN: 978-3-319-64018-1

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