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Exercise Testing in Pediatric Dilated Cardiomyopathy

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Exercise Physiology for the Pediatric and Congenital Cardiologist

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Abstract

Dilated cardiomyopathy (DCM) is the most common cardiomyopathy in children, and its hallmark is left ventricular (LV) dilation and systolic dysfunction. Impairment of exercise performance in children with DCM is due to a combination of inadequate tissue O2 delivery resulting from impaired heart rate and stroke volume increase with exercise and abnormalities in distribution or impedance to flow in pulmonary and peripheral circulations and of the skeletal muscle. Formal assessment of exercise performance is useful in identifying limitations and eliciting the mechanism of limitations in children with moderate and severe LV dysfunction and has a potential role in risk stratification of those with severe LV dysfunction.

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Author information

Authors and Affiliations

  1. Department of Pediatrics, Columbia University Medical College, New York, NY, USA

    Irene D. Lytrivi

  2. Program for Pediatric Cardiomyopathy, Heart Failure and Transplantation, Division of Pediatric Cardiology, Columbia Presbyterian Hospital, New York, NY, USA

    Irene D. Lytrivi

  3. Department of Pediatrics, Harvard Medical School, Boston, MA, USA

    T. P. Singh

  4. Heart Failure/Transplant Service, Department of Cardiology, Boston Children’s Hospital, Boston, MA, USA

    T. P. Singh

Authors
  1. Irene D. Lytrivi
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  2. T. P. Singh
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Corresponding author

Correspondence to Irene D. Lytrivi .

Editor information

Editors and Affiliations

  1. Department of Pediatrics, Harvard Medical School, Boston, MA, USA

    Jonathan Rhodes

  2. Department of Pediatrics, Harvard Medical School, Boston, MA, USA

    Mark E. Alexander

  3. Department of Pediatrics, Harvard Medical School, Boston, MA, USA

    Alexander R. Opotowsky

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Lytrivi, I.D., Singh, T.P. (2019). Exercise Testing in Pediatric Dilated Cardiomyopathy. In: Rhodes, J., Alexander, M., Opotowsky, A. (eds) Exercise Physiology for the Pediatric and Congenital Cardiologist. Springer, Cham. https://doi.org/10.1007/978-3-030-16818-6_22

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  • DOI: https://doi.org/10.1007/978-3-030-16818-6_22

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-16817-9

  • Online ISBN: 978-3-030-16818-6

  • eBook Packages: MedicineMedicine (R0)

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