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Scleroderma

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Pediatric Rheumatology for the Practitioner

Part of the book series: Comprehensive Manuals in Pediatrics ((CM PEDIATRICS))

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Abstract

The hallmark of the heterogeneous but related group of disorders called scleroderma is an area of hard, tight, inelastic (hide-bound) skin and subcutaneous tissue (Fig. 8.1).1,2 Fewer than 100 affected children have been reported on in the more than 130 years since the disorder was first described. The paucity of case reports does not reflect great rarity; one pediatric rheumatology clinic alone has reported 48 cases.3 It does reflect physician frustration: this disorder has been difficult to categorize; pathogenesis has defied understanding; treatment has been unsatisfactory.

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Authors and Affiliations

  1. Section of Pediatric Rheumatology Department of Pediatrics College of Physicians and Surgeons, Columbia University, New York, New York, USA

    Jerry C. Jacobs M.D. (Professor of Clinical Pediatrics, Director)

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  1. Jerry C. Jacobs M.D.
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© 1982 Springer Science+Business Media New York

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Jacobs, J.C. (1982). Scleroderma. In: Pediatric Rheumatology for the Practitioner. Comprehensive Manuals in Pediatrics. Springer, New York, NY. https://doi.org/10.1007/978-1-4757-6153-5_8

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  • DOI: https://doi.org/10.1007/978-1-4757-6153-5_8

  • Publisher Name: Springer, New York, NY

  • Print ISBN: 978-1-4757-6155-9

  • Online ISBN: 978-1-4757-6153-5

  • eBook Packages: Springer Book Archive

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