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Dilated, Restrictive/Infiltrative, and Hypertrophic Cardiomyopathies

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MGH Cardiology Board Review

Abstract

Cardiomyopathies represent a heterogeneous group of heart muscle diseases that are a major cause of morbidity and mortality. Classification schemes for cardiomyopathy have been complex, and efforts have been made to classify the disease states based on myocardial characteristics and etiologies. The etiology, diagnosis, and management of dilated cardiomyopathy (DCM), restrictive/infiltrative cardiomyopathy, and hypertrophic cardiomyopathy (HCM) are the subject of this chapter and several features of each form of cardiomyopathy are highlighted in Table 17-1.

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Abbreviations

ACE:

Angiotensin converting enzyme

AF:

Atrial fibrillation

ANA:

Anti-nuclear antibody

AR:

Aortic regurgitation

ARB:

Angiotensin receptor blocker

ARVC:

Arrhythmogenic right ventricular cardiomyopathy

BNP:

B-type natriuretic peptide

CAD:

Coronary artery disease

CMV:

Cytomegalovirus

CRT:

Cardiac resynchronization therapy

CT:

Computed tomography

CXR:

Chest x-ray

DCM:

Dilated cardiomyopathy

E’:

Early peak diastolic tissue velocity

ECG:

Electrocardiogram

HCM:

Hypertrophic cardiomyopathy

HIV:

Human immunodeficiency virus

HOCM:

Hypertrophic obstructive cardiomyopathy

ICD:

Implantable cardioverter defibrillator

LV:

Left ventricle or left ventricular

LVEF:

Left ventricular ejection fraction

LVH:

Left ventricular hypertrophy

LVOT:

Left ventricular outflow tract

MR:

Mitral regurgitation

MRI:

Magnetic resonance imaging

NTproBNP:

N-terminal pro B-type natriuretic peptide

RV:

Right ventricle or right ventricular

SAM:

Systolic anterior motion

SCD:

Sudden cardiac death

SPEP:

Serum protein electrophoresis

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DCM (AVI 14959 kb)

Amyloid (AVI 17528 kb)

HCM (AVI 9632 kb)

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Weiner, R.B., Baggish, A.L., Baggish, A.L. (2014). Dilated, Restrictive/Infiltrative, and Hypertrophic Cardiomyopathies. In: Gaggin, H., Januzzi, Jr., J. (eds) MGH Cardiology Board Review. Springer, London. https://doi.org/10.1007/978-1-4471-4483-0_17

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  • DOI: https://doi.org/10.1007/978-1-4471-4483-0_17

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  • Publisher Name: Springer, London

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  • Online ISBN: 978-1-4471-4483-0

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