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© 2017

Pulmonary Hypertension in Adult Congenital Heart Disease

  • Konstantinos Dimopoulos
  • Gerhard-Paul Diller
Book

Part of the Congenital Heart Disease in Adolescents and Adults book series (CHDAA)

Table of contents

  1. Front Matter
    Pages i-xv
  2. Pathophysiology and Classification of Pulmonary Hypertension in Adult Congenital Heart Disease

    1. Front Matter
      Pages 1-1
    2. Konstantinos Dimopoulos, Elizabeth Orchard, Annalisa Angelini
      Pages 3-22
    3. Shahin Moledina, Paraskevi Theocharis
      Pages 61-68
    4. Konstantinos Dimopoulos, Claudia Montanaro, Gerhard-Paul Diller
      Pages 69-89
    5. Lars Idorn, Lars Søndergaard
      Pages 91-104
    6. Margarita Brida, Gerhard-Paul Diller
      Pages 105-117
  3. The Diagnosis of Pulmonary Hypertension in Adult Congenital Heart Disease

    1. Front Matter
      Pages 119-119
    2. Edward D. Nicol, Michael B. Rubens
      Pages 149-161
    3. Michael A. Quail, Sonya V. Babu-Narayan
      Pages 179-193
    4. Graham Stuart, Reza Ashrafi
      Pages 195-214
    5. Massimo Chessa
      Pages 215-226
  4. Management of Pulmonary Hypertension in Adult Congenital Heart Disease

    1. Front Matter
      Pages 227-227
    2. Heba Nashat, Samantha J. Fitzsimmons, Carl Harries, Konstantinos Dimopoulos, S. John Wort
      Pages 229-251

About this book

Introduction

This book is intended as a comprehensive, practically oriented reference on pulmonary hypertension within the context of adult congenital heart disease (ACHD). After an introductory chapter on pathophysiology, the various types of pulmonary hypertension that may be encountered in ACHD are discussed, highlighting the specifics observed within different patient categories. The diagnostic approach is then addressed in detail, and the last section of the book is devoted to management options, from conservative approaches to interventional treatment and the concept of treat and repair. Management in specific patient subjects, such as pregnant women, Fontan patients, and Down syndrome patients with Eisenmenger syndrome, is fully discussed, and guidance is also provided on palliative care. 

Pulmonary arterial hypertension related to congenital heart disease (PAH-CHD), despite significant similarities in lung pathohysiology, differs significantly from other types of PAH in terms of mechanism of onset, natural history and management. Mistakes and pitfalls in the management of patients with PAH-CHD are often related to a lack of knowledge or expertise in this condition. Pulmonary Hypertension in Adult Congenital Heart Disease will be a valuable resource and learning tool for all who care for patients with ACHD, both in tertiary practice and general cardiology.


Keywords

Eisenmenger Syndrome Fontan-type circulation congenital heart disease connective tissue disease management of Fontan patients segmental PAH systemic pulmonary shunts

Editors and affiliations

  • Konstantinos Dimopoulos
    • 1
  • Gerhard-Paul Diller
    • 2
  1. 1.Adult Congenital Heart Centre and Centre for Pulmonary HypertensionRoyal Brompton Hospital and Imperial CollegeLondonUnited Kingdom
  2. 2.University HospitalMünsterGermany

About the editors

Diller Gerhard, Royal Bromption Hospital, London, UK

Konstantinos Dimopoulos, Royal Bromption Hospital, London, UK

Bibliographic information

  • Book Title Pulmonary Hypertension in Adult Congenital Heart Disease
  • Editors Konstantinos Dimopoulos
    Gerhard-Paul Diller
  • Series Title Congenital Heart Disease in Adolescents and Adults
  • Series Abbreviated Title Congenital Heart Disease in Adolescents and Adults
  • DOI https://doi.org/10.1007/978-3-319-46028-4
  • Copyright Information Springer International Publishing AG 2017
  • Publisher Name Springer, Cham
  • eBook Packages Medicine Medicine (R0)
  • Hardcover ISBN 978-3-319-46026-0
  • Softcover ISBN 978-3-319-83424-5
  • eBook ISBN 978-3-319-46028-4
  • Series ISSN 2364-6659
  • Series E-ISSN 2364-6667
  • Edition Number 1
  • Number of Pages XV, 368
  • Number of Illustrations 36 b/w illustrations, 46 illustrations in colour
  • Topics Cardiology
    Cardiac Surgery
    Pneumology/Respiratory System
  • Buy this book on publisher's site
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