Systemic Fibroinflammatory Disorders

  • Augusto Vaglio

Part of the Rare Diseases of the Immune System book series (RDIS)

Table of contents

  1. Front Matter
    Pages i-xii
  2. Davide Martorana, Francesco Bonatti, Javier Martin
    Pages 1-16
  3. Domenico Corradi, Maria Nicastro
    Pages 33-51
  4. Jochen Zwerina
    Pages 71-80
  5. Luca Frulloni, Antonio Amodio
    Pages 81-90
  6. Federica Maritati, Gabriella Moroni, Augusto Vaglio
    Pages 101-115
  7. Maria L. Urban, Alessandra Palmisano
    Pages 117-126
  8. Giovanni M. Rossi, Giacomo Emmi
    Pages 127-135
  9. Eric F. H. van Bommel, Nienke van Putte-Katier
    Pages 137-153
  10. Julien Haroche, Davide Gianfreda, Fleur Cohen-Aubart
    Pages 155-172
  11. Nicolò Pipitone
    Pages 195-207
  12. Derrick J. Todd, Jonathan Kay
    Pages 209-237
  13. Back Matter
    Pages 239-243

About this book


This book provides detailed information on the nosology, pathology, pathogenesis, clinical presentation, diagnosis and treatment of fibro-inflammatory disorders, rare diseases that often display systemic organ involvement. Among the conditions considered are IgG4-related disease, sclerosing cholangitis, Hashimoto’s and Riedel’s thyroiditis, retroperitoneal fibrosis/chronic periaortitis, mediastinal fibrosis, Erdheim-Chester disease, gadolinium-induced fibrosis, and sclerosing mesenteritis. This group of entities is still poorly defined and is characterized by the common denominator of chronic inflammatory infiltrate admixed with abundant fibrosis. IgG4-related disease is the prototypical example. Systemic Fibroinflammatory Disorders is the first book to draw together information on these conditions. As these diseases often require an interdisciplinary approach, the book is addressed to specialists of different disciplines, especially internists, rheumatologists, nephrologists, clinical immunologists, and hematologists.


aortitis multifocal fibrosclerosis IgG4-related disease gadolinium-induced fibrosis pancreatitis retroperitoneal fibrosis thyroiditis

Editors and affiliations

  • Augusto Vaglio
    • 1
  1. 1.Department of NephrologyUniversity HospitalParmaItaly

Bibliographic information

  • DOI
  • Copyright Information Springer International Publishing Switzerland 2017
  • Publisher Name Springer, Cham
  • eBook Packages Medicine Medicine (R0)
  • Print ISBN 978-3-319-41347-1
  • Online ISBN 978-3-319-41349-5
  • Series Print ISSN 2282-6505
  • Series Online ISSN 2283-6403
  • Buy this book on publisher's site
Industry Sectors
Health & Hospitals
Internal Medicine & Dermatology