Hypoplastic Left Heart Syndrome

  • Jack Rychik
  • Gil Wernovsky

Part of the Developments in Cardiovascular Medicine book series (DICM, volume 246)

Table of contents

  1. Front Matter
    Pages i-xiii
  2. Samuel Parry, Sara J. Marder
    Pages 29-37
  3. Sarah Tabbutt, Gil Wernovsky
    Pages 69-87
  4. Thomas L. Spray
    Pages 89-103
  5. Gil Wernovsky, Doff B. McElhinney, Sarah Tabbutt
    Pages 105-128
  6. Tom R. Karl
    Pages 129-148
  7. J. William Gaynor
    Pages 149-166
  8. James M. Steven, Susan C. Nicolson
    Pages 167-191
  9. Jacqueline Kreutzer, Jonathan J. Rome
    Pages 193-228
  10. Rhonda Foltz, Kathryn M. Dodds
    Pages 229-240
  11. Timothy M. Hoffman, Thomas L. Spray
    Pages 241-250
  12. Robert Ryan Clancy
    Pages 251-272
  13. Mitchell I. Cohen
    Pages 273-288
  14. Ronn E. Tanel, Larry A. Rhodes
    Pages 307-328
  15. Steven Paridon
    Pages 329-346
  16. Jack Rychik
    Pages 347-359
  17. Jack Rychik, Gil Wernovsky
    Pages 393-405
  18. Back Matter
    Pages 417-425

About this book


Despite approximately 50 years of progress in the management of com­ plex congenital heart disease, hypoplastic left heart syndrome (HLHS) has been one of the last cardiac malformations to yield to effective surgical treat­ ment. The surgical therapies for hypoplastic left heart syndrome have evolved by two quite disparate routes. One approach has been the staged reconstruc­ tion operations utilizing an initial operation pioneered by many but developed by Dr. William Norwood and subsequently modified by many other investigators. The first stage reconstruction operation has been refined and standardized such that the majority of infants now proceed to second and third stage reconstruc­ tive operations culminating in a Pontan Kreutzer single ventricle physiology. An alternative surgical approach has been the development of neonatal and infant heart transplantation for HLHS. This approach also has had a signifi­ cant impact on the treatment of HLHS and other cardiac malformations and has been associated with good intermediate term results. Both of the thera­ peutic approaches devised for treatment of hypoplastic left heart syndrome have been effective and the outcomes are continuing to improve with each.


cardiovascular congenital heart disease diagnostics genetics growth heart heart transplantation transplantation

Editors and affiliations

  • Jack Rychik
    • 1
  • Gil Wernovsky
    • 1
  1. 1.Division of CardiologyChildren’s Hospital of PhiladelphiaPhiladelphiaUSA

Bibliographic information

  • DOI
  • Copyright Information Kluwer Academic Publishers 2003
  • Publisher Name Springer, Boston, MA
  • eBook Packages Springer Book Archive
  • Print ISBN 978-1-4613-4988-4
  • Online ISBN 978-1-4615-0253-1
  • Series Print ISSN 0166-9842
  • Buy this book on publisher's site
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Health & Hospitals
Internal Medicine & Dermatology