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American Journal of Clinical Dermatology

, Volume 4, Issue 11, pp 799–802 | Cite as

Cutaneous Psammomatous Melanotic Schwannoma

Non-Recurrence with Surgical Excision
  • Nadine Claessens
  • Olivier Heymans
  • Jorge E. Arrese
  • Roy Garcia
  • Bert Oelbrandt
  • Gérald E. Piérard
Case Reports

Abstract

Background: Melanotic schwannoma is a pigmented nerve tumor that may be located in the skin and express local aggressivity. This tumor may occur singly. It may also be part of the Carney complex which consists of various, but specific, tumors.

Objective: We report two cases of subcutaneous melanotic schwannoma localized on the trunk in two men aged 37 and 45 years.

Methods: Conventional histology and immunohistochemistry were performed.

Results: One melanotic schwannoma was associated with a cutaneous atypical myxoma and multiple melanocytic lesions, all being part of the Carney complex. The other case had no associated signs. In both cases, the melanotic schwannoma was completely excised and did not recur.

Conclusion: Melanotic schwannoma is rare and curable by surgery. It must not be confused with malignant melanoma and other pigmented neoplasms. The Carney complex should be carefully ruled out.

Keywords

Schwann Cell S100 Protein Neurofibroma Factor XIIIa Cardiac Myxoma 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

Notes

Acknowledgments

No sources of funding were used to assist in the preparation of this manuscript. The authors have no conflicts of interest that are directly relevant to the content of this manuscript.

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Copyright information

© Adis Data Information BV 2003

Authors and Affiliations

  • Nadine Claessens
    • 1
  • Olivier Heymans
    • 2
  • Jorge E. Arrese
    • 1
  • Roy Garcia
    • 1
    • 3
  • Bert Oelbrandt
    • 2
  • Gérald E. Piérard
    • 1
  1. 1.Department of DermatopathologyUniversity Hospital Sart TilmanLiègeBelgium
  2. 2.Department of Plastic and Reconstructive SurgeryUniversity Medical Center Sart TilmanLiègeBelgium
  3. 3.Department of DermatologyHospital Nacional Sur-este EssaludCuscoPeru

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