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Oral and dental health care and anesthesia for persons with fibrodysplasia ossificans progressiva

  • Burton L. Nussbaum
  • Zvi Grunwald
  • Frederick S. Kaplan
Fibrodysplasia Ossificans Progressiva

Abstract

Fibrodysplasia ossificans progressiva (FOP) is a devastating genetic disorder with profound oral and dental health care issues. Most patients with FOP eventually develop heterotopic ossification of the chewing muscles with resultant ankylosis of the temporom andibular joints. Preventive and restorative dental care, as well as endodontic, periodontic, and orthodontic care present therapeutic challenges to the dental practitioner, the anesthesiologist, and to the FOP patient throughout his or her life.

Key Words

Fibrodysplasia ossificans progressiva (FOP) dental health care oral health care anesthesia 

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Copyright information

© Humana Press Inc. 2005

Authors and Affiliations

  • Burton L. Nussbaum
    • 1
  • Zvi Grunwald
    • 2
  • Frederick S. Kaplan
    • 3
    • 4
  1. 1.Department of Pediatric DentistryThe University of Pennsylvania School of Dental MedicinePhiladelphia
  2. 2.Department of AnesthesiologyJefferson University College of MedicinePhiladelphia
  3. 3.Department of Onthopedic SurgeryThe University of Pennsylvania School of MedicinePhiladelphia
  4. 4.Department of MedicineThe University of Pennsylvania School of MedicinePhiladelphia

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