Oral and dental health care and anesthesia for persons with fibrodysplasia ossificans progressiva
Fibrodysplasia ossificans progressiva (FOP) is a devastating genetic disorder with profound oral and dental health care issues. Most patients with FOP eventually develop heterotopic ossification of the chewing muscles with resultant ankylosis of the temporom andibular joints. Preventive and restorative dental care, as well as endodontic, periodontic, and orthodontic care present therapeutic challenges to the dental practitioner, the anesthesiologist, and to the FOP patient throughout his or her life.
Key WordsFibrodysplasia ossificans progressiva (FOP) dental health care oral health care anesthesia
Unable to display preview. Download preview PDF.
- 2.Cohen RB, Hahn GV, Tabas J, et al. 1993 The natural history of heterotopic ossification in patients who have fibrodysplasia ossificans progressiva. J Bone Joint Surg 75-A:215–219.Google Scholar
- 3.Rocke DM, Zasloff M, Peeper J, Cohen RB, Kaplan FS. 1994 Age and joint-specific risk of initial heterotopic ossification in patients who have fibrodysplasia ossificans progessiva. Clin Orthop Rel Res 301:243–248.Google Scholar
- 4.Kaplan FS, Shore EM, Connor JM. 2002 Fibrodysplasia ossificans progressiva (FOP). In: Royce PM, Steinmann B, eds. Connective Tissue and Its Heritable Disorders: Molecular, Genetic, and Medical Aspects, 2nd Ed. Wiley-Liss: John Wiley & Sons, New York, pp. 827–840.Google Scholar
- 10.Nussbaum BL, O'Hara I, Kaplan FS. 1996 Fibrodysplasia ossificans progressiva: report of a case with guidelines for pediatric dental and anesthetic management. J Dentistry Children 63:448–450.Google Scholar