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Evolving Perspectives on Congenital Glaucoma

  • Diagnosis and Monitoring of Glaucoma (R. Kuchtey, Section Editor)
  • Published:
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Abstract

Congenital glaucoma differs from adult glaucoma in that it represents a panocular disorder defined by structural, functional, and physiologic parameters. In order to achieve excellent visual outcomes, the management of congenital glaucoma involves concurrently controlling intraocular pressure and treating amblyopia, while minimizing any influence of a compromised visual axis. Thus far, difficulty in assessing visual function in pre-verbal children has resulted in a paucity of long-term visual outcome data. However, based on commonly recognized obstacles to structural/physiologic stability and functional rehabilitation status, we propose a congenital glaucoma severity scale in order to provide a cross-sectional stratification of disease severity. As the severity of pathology evolves over time, the severity score should be adjusted accordingly. The initial score and rate of changes in severity (“severity slope”) will help in prognosticating outcome. Future studies will be required to validate, calibrate, and discriminate this severity scale before clinical and research applications.

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Disclosure

Dr. Chang reports other from Retrophin Inc, other from Entopsis, LLC, grants from American Glaucoma Society, outside the submitted work. Dr. Grajewski and Dr. Cavuoto has nothing to disclose.

Human and Animal Rights and Informed Consent

This article contains no studies with human or animal subjects performed by the author.

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Authors and Affiliations

  1. Bascom Palmer Eye Institute, 900 NW 17th Street, Miami, FL, 33136, USA

    Ta C. Chang, Alana L. Grajewski & Kara M. Cavuoto

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  1. Ta C. Chang
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  2. Alana L. Grajewski
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  3. Kara M. Cavuoto
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Correspondence to Ta C. Chang.

Additional information

This article is part of the Topical Collection on Diagnosis and Monitoring of Glaucoma.

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Chang, T.C., Grajewski, A.L. & Cavuoto, K.M. Evolving Perspectives on Congenital Glaucoma. Curr Ophthalmol Rep 3, 85–90 (2015). https://doi.org/10.1007/s40135-015-0065-9

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  • DOI: https://doi.org/10.1007/s40135-015-0065-9

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