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Ewing’s Sarcoma with Extension into Superior Vena Cava and Right Atrium

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Indian Journal of Surgical Oncology Aims and scope Submit manuscript

Abstract

Ewing sarcoma is rarely shown to develop this intravascular extension so the decision of the initial treatment is more difficult. We report a 7-year-old boy of this sarcoma with extension into superior vena cava (SVC) and right atrium (RA), who was successfully treated with initial surgery. Intravascular extension was observed from the azygous vein to SVC and finally RA. The removal of the intravascular extension was done, 7 days before chemotherapy was started. The initial surgery for the intravascular extension may have decreased a risk of pulmonary tumor embolism and this made the chemotherapy done safe in this patient.

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Acknowledgments

We would like to thank the members of the department of cardiovascular surgery for their participation in the operation and we also thank Mr. James R. Valera for English proofreading.

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Authors and Affiliations

  1. Department of General Pediatrics, Tokyo Metropolitan Children’s Medical Center, 2-8-29, Musashidai, Fuchu-shi, Tokyo, 083-8561, Japan

    Yukari Atsumi & Hiroshi Hataya

  2. Department of Hematology and Oncology, Tokyo Metropolitan Children’s Medical Center, 2-8-29, Musashidai, Fuchu-shi, Tokyo, 083-8561, Japan

    Yuya Saito & Yuki Yuza

  3. Department of Pathology, Tokyo Metropolitan Children’s Medical Center, 2-8-29, Musashidai, Fuchu-shi, Tokyo, 083-8561, Japan

    Ryuji Fukuzawa

Authors
  1. Yukari Atsumi
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  2. Yuya Saito
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  3. Hiroshi Hataya
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  4. Ryuji Fukuzawa
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  5. Yuki Yuza
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Correspondence to Yukari Atsumi.

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Atsumi, Y., Saito, Y., Hataya, H. et al. Ewing’s Sarcoma with Extension into Superior Vena Cava and Right Atrium. Indian J Surg Oncol 10, 98–100 (2019). https://doi.org/10.1007/s13193-018-0849-0

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  • DOI: https://doi.org/10.1007/s13193-018-0849-0

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