Primary pericardial angiosarcoma is a rare malignant cardiac neoplasm with early metastasis and poor prognosis. There are currently no guidelines or effective therapeutic strategies. Here we report a case of a 22-year-old man who presented with chest pain, suffocation and transient syncope over the course of 4 months. Further workup showed a large mass in the right pericardium, histopathologic examination revealed angiosarcoma. The patient subsequently received a total of 8 cycles of chemotherapy (paclitaxel and doxorubicin). This patient has an overall survival of 1 year to date. The current examination methods and reported cases revealed that early detection of primary pericardial angiosarcoma with imaging examinations is critical for prognosis.
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Median overall survival
Positron emission tomography
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Wencui Li, Lizhu Han and Zhaoxiang Ye declare that they have nothing to disclose.
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Li, W., Han, L. & Ye, Z. Primary pericardial angiosarcoma: A case report. J. Nucl. Cardiol. (2021). https://doi.org/10.1007/s12350-020-02470-0
- Primary pericardial angiosarcoma