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Low-Grade Fibromyxoid Sarcoma of the External Auditory Canal: A Rare Pathology and Unusual Location

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Abstract

Low-grade fibromyxoid sarcoma (LGFMS) is an enigmatic soft tissue tumor. It frequently presents as a deeply seated mass in the proximal extremities and trunk. Superficial LGFMSs of the head and neck are exceedingly rare. Hyalinizing spindle cell tumor with giant rosettes (HSTGR) is an entity considered to be on the histologic spectrum of LGFMS. We present a case of a 44-year-old female who presented with a superficial, polypoid mass of the external auditory meatus. Microscopic examination revealed the classic histologic features of HSTGR. To our knowledge, this case is the first described at this extremely unusual location. Identification and reporting of such unusual cases is important to understand and compare the behavior of superficial LGFMS to that of the more common deeply seated tumors.

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Authors and Affiliations

  1. Department of Pathology, All India Institute of Medical Sciences, New Delhi, India

    Kalpana Kumari, Mehar C. Sharma & Geetika Singh

  2. Department of Otorhinolaryngology, All India Institute of Medical Sciences, New Delhi, India

    Ramya Thota & Alok Thakar

  3. Department of Radiology, All India Institute of Medical Sciences, New Delhi, India

    Heera Lal Chaudhary

  4. Department of Pathology, All India Institute of Medical Sciences, Room No. 1048, First Floor, Teaching Block, New Delhi, 110029, India

    Geetika Singh

Authors
  1. Kalpana Kumari
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  2. Ramya Thota
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  3. Heera Lal Chaudhary
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  4. Mehar C. Sharma
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  5. Alok Thakar
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  6. Geetika Singh
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Correspondence to Geetika Singh.

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Kumari, K., Thota, R., Chaudhary, H.L. et al. Low-Grade Fibromyxoid Sarcoma of the External Auditory Canal: A Rare Pathology and Unusual Location. Head and Neck Pathol 14, 276–282 (2020). https://doi.org/10.1007/s12105-019-01030-4

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  • DOI: https://doi.org/10.1007/s12105-019-01030-4

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