Abstract
Congenital chylothorax is a relatively uncommon condition seen in newborn period. Treatment comprises of adequate pleural fluid drainage, octreotide infusion, total parenteral nutrition followed by medium chain triglyceride (MCT) based low fat milk preparations. The authors present a case of Cornelia de Lange syndrome with a rare presentation of antenatally diagnosed chlyothorax presenting at birth with respiratory distress. The baby was managed with skimmed milk formulation fortified with coconut oil providing low fat and high proteins.
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AG managed and wrote the case report. KN contributed to patient management, case report writing and proof reading the report. AS, AP and GG contributed intellectually, helped in patient management and writing the manuscript. KM helped in patient management. MP managed the patient’s mother antenatally. GG is the guarantor for this article.
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Gupta, A., Naranje, K.M., Singh, A. et al. Congenital Chylothorax in a Neonate with Cornelia de Lange Syndrome: A Rare Complication Managed with a Novel Indigenously Prepared Milk Formulation. Indian J Pediatr 86, 645–647 (2019). https://doi.org/10.1007/s12098-019-02908-5
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DOI: https://doi.org/10.1007/s12098-019-02908-5