Maxillary Melanotic Neuroectodermal Tumour of Infancy Managed by Local Excision

Abstract

Tumours of the children involving the head and neck region are seen infrequently. Melanotic Neuroectodermal Tumor is an uncommon tumour of infancy involving the head and neck region typically. The case report describes a cheek swelling in an infant which on investigation was confirmed to be a Maxillary Melanotic Neuroectodermal tumour, subsequently subjected to excision and doing well on follow up.

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Acknowledgement

Dr Sreerekha, Associate Professor Pathology, contributed to the diagnosis by providing valuable inputs.

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Correspondence to Krishna Kumar Govindarajan.

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Shenoy, A., Penumadu, P., Meethale Thiruvoth, F. et al. Maxillary Melanotic Neuroectodermal Tumour of Infancy Managed by Local Excision. Indian J Otolaryngol Head Neck Surg (2021). https://doi.org/10.1007/s12070-021-02446-7

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Keywords

  • Melanotic neuroectodermal tumour
  • Progonoma
  • Small blue round cell tumour
  • Maxillary neoplasm
  • Pediatric tumour