Midline Congenital Upper Lip Sinus: A Rare Case

  • Falak Chowdhary
  • Aniece Chowdhary
  • Zoya Chowdhary
  • Aamir Chowdhary
Clinical Report


To present a rare case of a midline congenital upper lip sinus and its management. Background: A lip sinus is a rare condition, where a failure of the complete union during early stages of development leads to its formation. The prevalence of lower lip sinus is estimated to be about 0.00001% of the white population and that of upper lip sinus is even rarer. A congenital lip sinus maybe associated with syndromes such as; Von der Woude syndrome, or maybe present in isolation. A 25-year-old male presented to our clinic with intermittent swelling in the upper lip region. Clinical examination revealed a congenital midline lip sinus in the upper lip region, which had no intra-oral communication, and was managed by surgical excision. Till date, there has been a hand full of case reports of upper lip sinuses and fistulae, out of which only few are reported in India. We herein report a case of congenital upper lip sinus presenting as an intermittent swelling of the upper lip with its successful surgical management.


Congenital Lip sinus Midline Upper lip pit 


Compliance with Ethical Standards

Conflict of interest

The authors declare that they have no conflict of interest.


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Copyright information

© Association of Otolaryngologists of India 2018

Authors and Affiliations

  1. 1.ENT ClinicJammuIndia
  2. 2.Indira Gandhi Government Dental College and HospitalJammuIndia

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