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Diagnostic and Therapeutic Approach to Arrhythmias in Adult Congenital Heart Disease

  • Arrhythmia (R Kabra, Section Editor)
  • Published:
Current Treatment Options in Cardiovascular Medicine Aims and scope Submit manuscript

Abstract

Purpose of review

Adult survivors of congenital heart disease (CHD) are at increased risk of arrhythmia. The goal of this review is to outline diagnostic and therapeutic approaches to arrhythmia in adult CHD patients.

Recent findings

Macro-reentrant atrial tachyarrhythmia is the most common arrhythmia encountered in adults with CHD. Approximately 25% of hospitalizations associated with arrhythmia. The risk of ventricular arrhythmia is estimated as high as 25–100 times that for the general population and increased after two decades.

Summary

Routine ambulatory monitoring is important for arrhythmia risk assessment in adults with CHD. There are limitations, potential adverse effects, and risk of recurrence with antiarrhythmic drugs, catheter ablation, and surgical approaches. Adults with CHD suffer various forms of arrhythmia, are at increased risk of sudden death, and require special consideration for medical and interventional therapy.

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  1. Le Bonheur Children’s Hospital, The Heart Institute, 49 N Dunlap, 3rd Floor, Memphis, TN, 38103, USA

    Karine Guerrier DO, MPH, Benjamin Hendrickson MD, B. Rush Waller MD & Glenn T. Wetzel MD, PhD

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  1. Karine Guerrier DO, MPH
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  2. Benjamin Hendrickson MD
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  3. B. Rush Waller MD
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  4. Glenn T. Wetzel MD, PhD
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Correspondence to Karine Guerrier DO, MPH.

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This article is part of the Topical Collection on Arrhythmia

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Guerrier, K., Hendrickson, B., Waller, B.R. et al. Diagnostic and Therapeutic Approach to Arrhythmias in Adult Congenital Heart Disease. Curr Treat Options Cardio Med 21, 44 (2019). https://doi.org/10.1007/s11936-019-0749-9

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  • DOI: https://doi.org/10.1007/s11936-019-0749-9

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