Chiari Headache

  • Amit Mehta
  • Priyanka Chilakamarri
  • Adeel Zubair
  • Deena Kuruvilla
Uncommon and/or Unusual Headaches and Syndromes (J Ailani, Section Editor)
Part of the following topical collections:
  1. Topical Collection on Uncommon and/or Unusual Headaches and Syndromes


Purpose of Review

Chiari malformations (CM) are a group of neuroanatomical pathologies resulting from overcrowding of the hindbrain. The purpose of this review is to characterize Chiari headache (CH) and describe diagnosis and treatment of the condition.

Recent Findings

Recent research has helped solidify the criteria for diagnosis of CH. Imaging studies have expanded our understanding of the morphological features producing them and helped to better characterize the pathophysiology. Additionally, identifying this unusual headache disorder accurately has helped with specific treatment options.


CH is a disabling condition which can effect multiple domains of a patient’s life. The diagnostic criteria has improved, and we now have a better understanding of the pathophysiology and imaging findings associated with CH. Future research is warranted to find new treatment options for individuals suffering from this condition.


Chiari headache Chiari malformation Syringomyelia Chiari type I Occipital headache Headache 


Compliance with Ethical Standards

Conflict of Interest

Amit Mehta, Priyanka Chilakamarri, and Adeel Zubair declare no conflict of interest. Deena Kuruvilla has been a speaker for Amgen Migraine program and a Neurology consultant for GLG consulting group, both outside of this work.

Human and Animal Rights and Informed Consent

This article does not contain any studies with human or animal subjects performed by any of the authors.


Papers of particular interest, published recently, have been highlighted as: • Of importance •• Of major importance

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Copyright information

© Springer Science+Business Media, LLC, part of Springer Nature 2018

Authors and Affiliations

  • Amit Mehta
    • 1
  • Priyanka Chilakamarri
    • 1
  • Adeel Zubair
    • 1
  • Deena Kuruvilla
    • 1
  1. 1.Department of NeurologyYale School of MedicineNew HavenUSA

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