Surgical repair of an isolated left-sided partial anomalous pulmonary venous connection in an 18-month-old child


The isolated left-sided partial anomalous pulmonary venous connection is a rare congenital anomaly. Only 3% of cases have been reported with drainage from the whole left lung into the left innominate vein. This anomaly is often asymptomatic and may go undetected (particularly in non-referral centers) until adulthood when symptoms begin to manifest. Transthoracic echocardiography is the main diagnostic tool; however, computed tomography angiography, and magnetic resonance imaging are widely used nowadays. Herein, we present the case of an 18-month-old girl with the diagnosis of isolated left-sided partial anomalous pulmonary venous connection as the left pulmonary veins were draining into the left innominate vein via a vertical vein. The patient underwent surgical repair by anastomosing the vertical vein to the left atrial appendage using cardiopulmonary bypass and cardiac arrest. The patient was discharged on the fifth day without complications. The precise follow-up for 12 months showed improved clinical symptoms, and the successively performed TTE confirmed the excellent result of the operation.

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  1. 1.

    Javangula K, Cole J, Cross M, Kay PH. An unusual manifestation of left partial anomalous pulmonary venous connection. Interact Cardiovasc Thorac Surg. 2010;11:846–8.

    Article  Google Scholar 

  2. 2.

    Göksel OS, Torlak Z, El H, Alkara U, Tireli E, Dayioğlu E. Isolated partial anomalous pulmonary venous connection of the left lung. Heart Surg Forum. 2009;12(3):E182–183.

    Article  Google Scholar 

  3. 3.

    Ammannaya GKK, Mishra P, Khandekar JV. Left sided PAPVC with intact IAS—Surgically managed with vertical vein anastomosis to LA appendage: a rare case report. Int J Surg Case Rep. 2019;59:217–9.

    Article  Google Scholar 

  4. 4.

    Wang TL, Hung HF, Lin C, Hsiung MC, Wei J. Multiple anomalous left pulmonary venous connections detected with transthoracic echocardiography. J Cardiothorac Surg. 2013;17(8):130.

    Article  Google Scholar 

  5. 5.

    Khalil C, Mosleh W, Ibrahim A, Young H, Corbelli J. A partial anomalous pulmonary venous connection in a severely symptomatic patient, is surgery always recommended? Cureus. 2018;10(7):e2962.

    PubMed  PubMed Central  Google Scholar 

  6. 6.

    Edwin F. Left-sided partial anomalous pulmonary venous connection—should diagnosis lead to surgery? Interact Cardiovasc Thorac Surg. 2010;11:847–8.

    Article  Google Scholar 

  7. 7.

    Ammash NM, Seward JB, Warnes CA, Connolly HM, O’Leary PW, Danielson GK. Partial anomalous pulmonary venous connection: diagnosis by transesophageal echocardiography. J Am Coll Cardiol. 1997;29:1351–8.

    CAS  Article  Google Scholar 

  8. 8.

    Lyen S, Wijesuriya S, Ngan-Soo E, et al. Anomalous pulmonary venous drainage: a pictorial essay with a CT focus. J Congenit Heart Dis. 2017;1:7.

    Article  Google Scholar 

  9. 9.

    Sachweh JS, Daebritz SH, Hermanns B, Fausten B, Jockenhoevel S, Handt S, et al. Hypertensive pulmonary vascular disease in adults with secundum or sinus venosus atrial septal defect. Ann Thorac Surg. 2006;81:207–13.

    Article  Google Scholar 

  10. 10.

    ElBardissi AW, Dearani JA, Suri RM, Danielson GK. Left-sided partial anomalous pulmonary venous connections. Ann Thorac Surg. 2008;85:1007–144.

    Article  Google Scholar 

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Correspondence to Alwaleed Al-Dairy.

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Al-Dairy, A., Al-kyakhi, L., Al-mithiab, L. et al. Surgical repair of an isolated left-sided partial anomalous pulmonary venous connection in an 18-month-old child. Gen Thorac Cardiovasc Surg (2020).

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  • Partial anomalous pulmonary venous connection
  • Congenital heart defect