General Thoracic and Cardiovascular Surgery

, Volume 65, Issue 11, pp 650–652 | Cite as

Challenging mitral valve repair for double-orifice mitral valve with noncompaction of left ventricular myocardium

  • Manabu Yamasaki
  • Hiroyasu Misumi
  • Kohei Abe
  • Kohei Kawazoe
Case Report


Double-orifice mitral valve (DOMV) is a relatively rare cardiac anomaly. Although usually associated with various cardiac anomalies, co-presence of DOMV and noncompaction of left ventricular myocardium (NCLVM) is extremely rare. Here, we present a 24-year-old male who underwent mitral valve repair using artificial chordae and annuloplasty at the posterior commissure for severe mitral regurgitation (MR), resulting from flail anterior leaflet of the larger postero-medial orifice and dilatation of left ventricle with NCLVM. One year later, he underwent second mitral valve repair for recurrence of MR. Further endoscopic evaluation of the left ventricle, and reinforcement via artificial ring, enabled us to achieve repair.


Mitral valve repair Mitral regurgitation Double orifice 


Compliance with ethical standards

Conflict of interest

Authors have nothing to disclose with regard to commercial support.


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Copyright information

© The Japanese Association for Thoracic Surgery 2017

Authors and Affiliations

  • Manabu Yamasaki
    • 1
  • Hiroyasu Misumi
    • 1
  • Kohei Abe
    • 1
  • Kohei Kawazoe
    • 1
  1. 1.Department of Cardiovascular SurgerySt. Luke’s International HospitalTokyoJapan

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