Oral Radiology

, Volume 34, Issue 2, pp 179–184 | Cite as

Gorham’s disease of the mandible: radiological features

  • Hui Yuh Soh
  • Azizah Ahmad Fauzi
  • Abd Jabar Nazimi
  • Roszalina Ramli
Case Report
  • 86 Downloads

Abstract

The most conspicuous element of Gorham’s disease is its radiographic features, wherein massive disappearance of the mandible is observed. We report a case of an adolescent boy with massive osteolysis of the mandible in whom the diagnosis of Gorham’s disease was made. A 14-year-old boy was referred to the Department of Oral and Maxillofacial Surgery, Universiti Kebangsaan Malaysia Medical Centre, Kuala Lumpur, for the management of a massive mandibular deformity. He was diagnosed with a hemangioma-like lesion at 1 year of age. The disease had progressed for an unknown number of years. Plain X-rays and computed tomography images were examined for reconstructive surgery planning. Gorham’s disease is self-limiting, but has catastrophic results. The role of imaging is huge, particularly for reconstructive surgery planning.

Keywords

Gorham’s disease Radiological features Mandible 

Notes

Acknowledgements

We thank Dr. Kew Thean Yean, Department of Radiology, Universiti Kebangsaan Malaysia Medical Centre for his help with the imaging.

Compliance with ethical standards

Conflict of interest

Hui Yuh Soh, Azizah Ahmad, Abd Jabar Nazimi, and Roszalina Ramli declare that they have no conflict of interest.

Human rights statements

All procedures followed were in accordance with the ethical standards of the responsible committee on human experimentation (institutional and national) and with the Helsinki Declaration of 1964 and later versions.

Informed consent

Informed consent was obtained from the patient (now aged above 21 years) for being included in the study.

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Copyright information

© Japanese Society for Oral and Maxillofacial Radiology and Springer Japan 2017

Authors and Affiliations

  • Hui Yuh Soh
    • 1
  • Azizah Ahmad Fauzi
    • 2
  • Abd Jabar Nazimi
    • 1
  • Roszalina Ramli
    • 1
  1. 1.Department of Oral and Maxillofacial SurgeryUniversiti Kebangsaan Malaysia Medical CentreKuala LumpurMalaysia
  2. 2.Department of Clinical Oral Biology, Faculty of DentistryUniversiti Kebangsaan MalaysiaKuala LumpurMalaysia

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