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Pituitary

, Volume 13, Issue 2, pp 176–182 | Cite as

Recurrent pituitary ependymoma: a complex clinical problem

  • Rosie Belcher
  • Harvinder S. Chahal
  • Jane Evanson
  • Farhad Afshar
  • Silvia Marino
  • Ashley B. Grossman
Case Report

Abstract

Ependymomas rarely arise from the region of the pituitary fossa, with only four cases previously reported in the literature. We present a complex case of a recurrent ependymoma of the parasellar region which has been difficult to clinically manage due to its tendency to recurrence. Our patient has had four operations over the last 28 years, with external beam radiotherapy, but still has residual tumor and is currently panhypopituitary and with significant visual loss. We believe there is considerable uncertainty as to the optimal management of any future progression, which seems likely, and are currently considering the use of radiosurgery with careful sparing of the optic chiasm, or possibly the chemotherapeutic agent temozolomide. Our case emphasises the recurrent nature of this rare but difficult tumor.

Keywords

Ependymoma Pituitary tumor Radiotherapy 

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Copyright information

© Springer Science+Business Media, LLC 2008

Authors and Affiliations

  • Rosie Belcher
    • 1
  • Harvinder S. Chahal
    • 1
  • Jane Evanson
    • 2
  • Farhad Afshar
    • 3
  • Silvia Marino
    • 4
  • Ashley B. Grossman
    • 5
  1. 1.Department of EndocrinologyBarts and the London School of MedicineLondonUK
  2. 2.Department of RadiologyBarts and the London School of MedicineLondonUK
  3. 3.Department of NeurosurgeryBarts and the London School of MedicineLondonUK
  4. 4.Department of HistopathologyBarts and the London School of MedicineLondonUK
  5. 5.Department of EndocrinologySt. Bartholomew’s HospitalLondonUK

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