Advertisement

International Ophthalmology

, Volume 34, Issue 4, pp 919–921 | Cite as

Spontaneous bilateral corneal perforation in a patient with ichthyosis

  • Yasin Cinar
  • Caferi Tayyar Selcuk
  • Abdullah Kursat Cingu
  • Fatih Mehmet Turkcu
  • Harun Yuksel
  • Adnan Yildirim
  • Tuba Cinar
Case Report

Abstract

We present an 8-month-old female patient with bilateral spontaneous corneal perforation and lamellar ichthyosis. On examination, the skin of the body and face of the patient was completely dry and scaly. Cicatricial ectropion and descemetocele with small perforations were seen. Double-layered amniotic membrane transplantation on the cornea with eyelid construction was performed on both eyes. At the 6-month follow-up, lower eyelid minimal ectropion formation and inferior corneal leukoma were seen bilaterally. In ichthyosis patients, the cornea should be monitored closely due to the risk of severe visual loss and corneal perforation.

Keywords

Spontaneous corneal perforation Ectropion Ichthyosis 

Notes

Conflicts of interest

None of the authors have any financial interests to disclose.

References

  1. 1.
    Uthoff D, Gorney M, Teichmann C (1994) Cicatricial ectropion in ichthyosis: a novel approach to treatment. Ophthal Plast Reconstr Surg 10:92–95PubMedCrossRefGoogle Scholar
  2. 2.
    Cruz AA, Menezes FA, Chaves R, Pinto Coelho R, Velasco EF, Kikuta H (2000) Eyelid abnormalities in lamellar ichthyoses. Ophthalmology 107:1895–1898PubMedCrossRefGoogle Scholar
  3. 3.
    Jay B, Blach RK, Wells RS (1968) Ocular manifestations of ichthyosis. Br J Ophthalmol 52:217–226PubMedCentralPubMedCrossRefGoogle Scholar
  4. 4.
    Menke TB, Moschner S, Joachimmeyer E, Ahrens P, Geerling G (2006) Congenital ectropion in ichthyosis congenita mitis and gravis. Ophthalmologe 103:410–415PubMedCrossRefGoogle Scholar
  5. 5.
    Ozgur OR, Akcay L, Tutas N, Ozkurt Y (2011) Cicatricial upper and lower eyelid ectropion in an ichthyosis patient surgical correction. J Dermatol Case Rep 5:27–29PubMedCentralPubMedCrossRefGoogle Scholar
  6. 6.
    Hosal BM, Abbasogglu OE, Gursel E (1999) Surgical treatment of cicatricial ectropion in lamellar ichthyosis. Orbit 19:37–40PubMedCrossRefGoogle Scholar
  7. 7.
    Chaudhary M, Shrestha GB, Keyal A (2013) Lamellar ichthyosis presenting as bilateral spontaneous corneal perforation. Nepal J Ophthalmol 5:117–119PubMedGoogle Scholar
  8. 8.
    Turgut B, Aydemir O, Kaya M, Turkcuoglu P, Demir T, Celiker U (2009) Spontaneous corneal perforation in a patient with lamellar ichthyosis and dry eye. Clin Ophthalmol 3:611–613PubMedCentralPubMedCrossRefGoogle Scholar
  9. 9.
    Eltutar K, Karadede S, Atlihan F, Ozler S (1988) Ectropion and bilateral corneal perforation in a case of congenital ichthyosiform erythroderma. Clinical and histopathologic review. Ophtalmologie 2:253–254PubMedGoogle Scholar

Copyright information

© Springer Science+Business Media Dordrecht 2013

Authors and Affiliations

  • Yasin Cinar
    • 1
  • Caferi Tayyar Selcuk
    • 1
  • Abdullah Kursat Cingu
    • 1
  • Fatih Mehmet Turkcu
    • 1
  • Harun Yuksel
    • 1
  • Adnan Yildirim
    • 1
  • Tuba Cinar
    • 2
  1. 1.Dicle UniversityDiyarbakirTurkey
  2. 2.Diyarbakir Çocuk HastanesiDiyarbakirTurkey

Personalised recommendations