International Ophthalmology

, Volume 32, Issue 2, pp 199–201 | Cite as

Bilateral Marcus Gunn jaw winking synkinesis with monocular elevation deficiency: a case report and literature review

Case Report


Marcus Gunn jaw winking synkinesis (MGJWS) occurs due to an aberrant innervation of the levator palpebrae superioris muscle by a branch of the motor division of the trigeminal nerve that supplies the muscles of mastication. MGJWS is mostly unilateral occurring in isolation and is less frequently associated with ocular or systemic abnormalities. Although MGJWS is mostly unilateral, few bilateral cases have been reported. Here we describe a rare case of bilateral MGJWS in an 18 year-old male patient with asymmetric bilateral ptosis and monocular elevation deficiency in the right eye.


Congenital ptosis Marcus Gunn jaw winking synkinesis Monocular elevation deficiency Hypotropia 


Conflict of interest


Supplementary material

Online supplement 1: Video of the patient showing ‘see-saw’ movement of the upper eyelids on side-to-side movements of the jaw (MPG 9120 kb)


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Copyright information

© Springer Science+Business Media B.V. 2012

Authors and Affiliations

  • Akash D. Shah
    • 1
  • Anand B. Kumar
    • 2
  • Kulin Kothari
    • 3
  1. 1.Department of Orbit and OculoplastyBombay City Eye Institute and Research CentreMumbaiIndia
  2. 2.Department of Paediatric Ophthalmology and Adult StrabismusBombay City Eye Institute and Research CentreMumbaiIndia
  3. 3.Chairman and Medical Director, Bombay City Eye Institute and Research CentreMumbaiIndia

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