Concomitant Heterotopic Pancreas and Endometriosis as a Rare Cause of Ileo-Ileal Intussusception in a Young Woman with Spina Bifida: Case Report and Literature Review



Isolated heterotopic pancreas (HP) as the primary cause of bowel intussusception is extremely rare. We report a case of a 33-year-old female patient with spina bifida admitted to the Emergency Surgical Department for ileal intussusception due to the presence of heterotopic pancreas associated with endometriosis.

Areas Covered

Symptomatic ileal intussusception for ectopic pancreas is usually associated with overt gastrointestinal blood loss (predominantly melena), abdominal pain, vomiting, and weight loss. Treatment is universally surgical.

Expert Commentary

Isolated heterotopic pancreas is a rare condition; it should be considered in the differential diagnosis of bowel intussusception.

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Computed tomography


Esophago-gastro-duodenal endoscopy




White blood cells


C-reactive protein


Heterotopic pancreas


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Correspondence to A. Lauro.

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Sciannamea, A., Vaccari, S., Marasco, G. et al. Concomitant Heterotopic Pancreas and Endometriosis as a Rare Cause of Ileo-Ileal Intussusception in a Young Woman with Spina Bifida: Case Report and Literature Review. Dig Dis Sci (2020).

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  • Heterotopic pancreas
  • Abdominal pain
  • Spina bifida
  • Endometriosis
  • Bowel Intussusception