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Sympathetic dysfunction of systemic right ventricle in congenitally corrected transposition of the great arteries

  • Yasushi Akutsu
  • Kyouichi Kaneko
  • Yusuke Kodama
  • Hui-Ling Li
  • Jumpei Suyama
  • Takehiko Gokan
  • Youichi Kobayashi
Case in Point

Abstract

We evaluate the systemic right ventricle (SRV) failure of congenitally corrected transposition of the great arteries using the scintigraphic studies in a case with 32-year-old male who improved the heart failure by the use of beta-adrenergic blockers. The myocardial perfusion sympathetic nervous system activity mismatch with preserved coronary flow and wall thickness indicates a distinctive feature as SRV cardiomyopathy, suggesting the importance of recovery of SRV sympathetic dysfunction for improving the prognosis.

Keywords

Corrected transposition of the great arteries Heart failure Systemic right ventricle Sympathetic nervous system 

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Copyright information

© Springer Science+Business Media, B.V. 2009

Authors and Affiliations

  • Yasushi Akutsu
    • 1
  • Kyouichi Kaneko
    • 1
  • Yusuke Kodama
    • 1
  • Hui-Ling Li
    • 1
  • Jumpei Suyama
    • 2
  • Takehiko Gokan
    • 2
  • Youichi Kobayashi
    • 1
  1. 1.Division of Cardiology, Department of MedicineShowa University School of MedicineShinagawaku, TokyoJapan
  2. 2.Department of RadiologyShowa University School of MedicineTokyoJapan

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