Scimitar syndrome; an unusual congenital abnormality occasionally seen in adults
Scimitar syndrome a very rare and variable congenital disorder characterized by an anomalous connection of the pulmonary vein with the IVC. The syndrome is mostly seen in very early infancy, but was now recognized in a 46-year-old woman, who was referred to the outpatient clinic of the department of cardiology with complaints of dizziness. Contrast enhanced computer tomography (CT) showed dextroposition of the heart and a large right pulmonary vein joined the inferior vena cava (IVC) just above the level of the diaphragm. The typical features of the syndrome are discussed.
Keywordscardiac CT congenital heart disease scimitar syndrome
Unable to display preview. Download preview PDF.
- 2.Cooper G. (1836) Case of malformation of the thoracic viscera consisting of imperfect development of the right lung and transposition of the heart. London Med Gaz 18:600–601Google Scholar
- 3.Neill CA, Ferenza C, Sabiston DC (1960) The familial occurrence of hypoplastic right lung with systemic arterial supply and venous return, ‘scimitar syndrome’. Bull John Hopkins Hosp 107:1–21Google Scholar