Scimitar syndrome; an unusual congenital abnormality occasionally seen in adults

  • R.J.P. Haest
  • C.J.M. van den  Berg
  • R. Goei
  • L.H.B. Baur


Scimitar syndrome a very rare and variable congenital disorder characterized by an anomalous connection of the pulmonary vein with the IVC. The syndrome is mostly seen in very early infancy, but was now recognized in a 46-year-old woman, who was referred to the outpatient clinic of the department of cardiology with complaints of dizziness. Contrast enhanced computer tomography (CT) showed dextroposition of the heart and a large right pulmonary vein joined the inferior vena cava (IVC) just above the level of the diaphragm. The typical features of the syndrome are discussed.


cardiac CT congenital heart disease scimitar syndrome 


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Copyright information

© Springer Science+Business Media, Inc. 2006

Authors and Affiliations

  • R.J.P. Haest
    • 1
  • C.J.M. van den  Berg
    • 1
  • R. Goei
    • 2
  • L.H.B. Baur
    • 1
    • 3
  1. 1.Department of cardiologyAtrium medical centreHeerlenthe Netherlands
  2. 2.Department of radiologyAtrium medical centreHeerlenThe Netherlands
  3. 3.Department of cardiologyAtrium MC HeerlenHeerlenThe Netherlands

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