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A refractory hypertensive patient with fibromuscular dysplasia and multicystic dysplastic kidney

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Abstract

The case of a 16-year-old male patient with left renal artery stenosis due to fibromuscular dysplasia (FMD) and an atrophic kidney due to a right multicystic dysplastic kidney (MCDK) who presented with refractory hypertension is reported. On continuous Doppler imaging, the peak systolic velocity (PSV) at the stenotic site of the left renal artery was 404 cm/s. The FMD formed a “string-of-beads” appearance on computed tomographic angiography (CTA) and renal artery angiography. Percutaneous transluminal renal angioplasty (PTRA) with a balloon catheter was performed, after which the left renal artery returned to near normal, and his blood pressure decreased to within the normal range. In this case, the main cause of refractory hypertension was considered to have been renal artery stenosis due to left FMD.

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References

  1. Slovut DP, Olin JW. Fibromuscular dysplasia. N Engl J Med. 2004;350:1862–71.

    Article  CAS  PubMed  Google Scholar 

  2. Plouin PF, Perdu J, La Batide-Alanore A, et al. Fibromuscular dysplasia. Orphanet J Rare Dis. 2007;2:28.

    Article  PubMed  PubMed Central  Google Scholar 

  3. Narchi H. Risk of hypertension with multicystic kidney disease: a systematic review. Arch Dis Child. 2005;90:921–4.

    Article  CAS  PubMed  PubMed Central  Google Scholar 

  4. Gottsäter A, Lindblad B. Optimal management of renal artery fibromuscular dysplasia. Ther Clin Risk Manag. 2014;10:583–95.

    Article  PubMed  PubMed Central  Google Scholar 

  5. Rountas C, Vlychou M, Vassiou K, et al. Imaging modalities for renal artery stenosis in suspected renovascular hypertension: prospective intraindividual comparison of color Doppler US, CT angiography, GD-enhanced MR angiography, and digital subtraction angiography. Ren Fail. 2007;29:295–302.

    Article  CAS  PubMed  Google Scholar 

  6. Pickering T. Peripheral and renal vein renin testing. In: Novick A, Scoble J, Hamilton G, editors. Renal vascular disease. London: WB Saunders; 1996. p. 185–93.

    Google Scholar 

  7. Prasad A, Zafar N, Mahmud E. Assessment of renal artery fibromuscular dysplasia: angiography, intravascular ultrasound (with virtual histology), and pressure wire measurements. Catheter Cardiovasc Intervent. 2009;74:260–4.

    Google Scholar 

  8. Bruyne BD, Manoharan G, Pijls NHJ, et al. Assessment of renal artery stenosis severity by pressure gradient measurements. J Am Coll Cardiol. 2006;48:1851–5.

    Article  PubMed  Google Scholar 

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Authors and Affiliations

  1. Department of Pediatrics, Iwate Medical University School of Medicine, 19-1 Uchimaru, Morioka, 020-8505, Japan

    Shin Takahashi, Yurie Takizawa, Satoshi Nakano & Kotaro Oyama

Authors
  1. Shin Takahashi
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  2. Yurie Takizawa
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  3. Satoshi Nakano
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  4. Kotaro Oyama
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Corresponding author

Correspondence to Shin Takahashi.

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The authors declare no conflicts of interest.

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Additional informed consent was obtained from the patient and his parents for whom identifying information is included in this article.

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Takahashi, S., Takizawa, Y., Nakano, S. et al. A refractory hypertensive patient with fibromuscular dysplasia and multicystic dysplastic kidney. J Med Ultrasonics 45, 657–660 (2018). https://doi.org/10.1007/s10396-018-0884-z

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  • DOI: https://doi.org/10.1007/s10396-018-0884-z

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