Abstract
Kaposiform hemangioendothelioma (KHE) is a rare vascular tumor of early childhood and infancy. Kasabach–Merritt phenomenon, a common complication of KHE, is characterized by life-threatening thrombocytopenia, hemolytic anemia, and consumption coagulopathy. There may be atypical cases that do not present with Kasabach–Merritt phenomenon and do have atypical imaging findings. Knowledge of atypical imaging features may assist radiologists in identifying KHE. In this report, we present a 4-year-old case of KHE with atypical ultrasound findings.
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References
Cabot RC, Harris NL, Shepard J-AO, Mulliken JB, Anupindi S, Alan R, et al. Case 13-2004: a newborn girl with a large cutaneous lesion, thrombocytopenia, and anemia. N Engl J Med. 2004;350:1764–75.
Dubois J, Garel L, David M, Powell J. Vascular soft-tissue tumors in infancy: distinguishing features on doppler sonography. AJR Am J Roentgenol. 2002;178:1541–5.
Croteau SE, Liang MG, Kozakewich HP, Alomari AI, Fishman SJ, Mulliken JB, et al. Kaposiform hemangioendothelioma: atypical features and risks of Kasabach–Merritt phenomenon in 107 referrals. J Pediatr. 2013;162:142–7.
Behr GG, Johnson C. Vascular anomalies: hemangiomas and beyond—Part I, fast-flow lesions. AJR Am J Roentgenol. 2013;200:414–22.
Ryu YJ, Choi YH, Cheon J-E, Kim WS, Kim I-O, Park JE, et al. Imaging findings of Kaposiform hemangioendothelioma in children. Eur J Radiol. 2017;86:198–205.
Calvo-Garcia MA, Kline-Fath BM, Adams DM, Gupta A, Koch BL, Lim F-Y, et al. Imaging evaluation of fetal vascular anomalies. Pediatr Radiol. 2015;45:1218–29.
Erdem Toslak I, Kilic KK, Cekic B, Cekic S, Yagci B. Epitheloid hemangioendothelioma of the ankle with unusual magnetic resonance imaging appearance. Diagn Interv Imaging. 2017;98:741–3.
Kaplan MC, Coleman BG, Shaylor SD, Howell LJ, Oliver ER, Horii SC, et al. Sonographic features of rare posterior fetal neck masses of vascular origin. J Ultrasound Med. 2013;32:873–80.
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All procedures performed were in accordance with the ethical standards of the responsible committee on human experimentation (institutional and national) and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.
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Erdem Toslak, I., Stegman, M., Reiter, M.P. et al. Atypically presenting kaposiform hemangioendothelioma of the knee: ultrasound findings. J Med Ultrasonics 45, 653–656 (2018). https://doi.org/10.1007/s10396-018-0878-x
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DOI: https://doi.org/10.1007/s10396-018-0878-x