Summary
Background
Solid pseudopapillary tumours, also known as Frantz’s tumours, are rare pancreatic lesions which usually occur in young 20–30 year-old women. They account for about 2% of all exocrine pancreatic tumours. They often present with vague abdominal pain and the diagnosis is frequently an incidental finding.
Methods
In this case series and narrative review, we attempt to update the current standpoint on primary pseudopapillary tumours. In this paper we present a case series of three subjects (2 females and 1 male) who were diagnosed with primary pseudopapillary tumours. Their treatment and follow-up is described in detail.
Results
These tumours will be discussed in the context of a literature review.
Conclusions
Surgical resection remains the primary method of treatment for this subtype of pancreatic tumours. The prognosis is excellent in patients who undergo resection.
This is a preview of subscription content, log in via an institution to check access.
References
Branco C, Vilaca S, Falcao J. Solid pseudopapillary neoplasm-Case report of a rare pancreatic tumor. Int J Surg Case Rep. 2017;33:148–50.
Rivera M, Lara-Del Rio JA, Di Pasquale-Guadalupe L, Zequeira J. Silent presentation of a solid pseudopapillary neoplasm of the pancreas. Am J Case Rep. 2017;18:656–9.
Cai H, Zhou M, Hu Y. Solid-pseudopapillary neoplasms of the pancreas: clinical and pathological features of 33 cases. Surg Today. 2013;43:148–54.
Bochis OV, Bota M, Mihut E, Buiga R, Hazbei DS, Irimie A. Solid pseudopapillary tumor of the pancreas: clinical-pathological features and management of 13 cases. Clujul Med. 2017;90(2):171–8.
Słowik-Moczydłowska Z, Gogolewski M, Yaqoub S. Solid pseudopapillary tumor of the pancreas (Frantz’s tumor): two case reports and a review of the literature. J Med Case Rep. 2015;9:268.
Chhadi TS, Deshpande AH, Chhadi SA, Kumbhalkar DT, Raut WK. A solid seudopapillary tumour of the head of pancreas: a rare case report diagnosed by fine needle aspiration cytology. J Clin Diagn Res. 2016;10(6):ED06–ED08.
Punch C, Garg N, Harris P. Recurrence of Solid Pseudopapillary Tumor: A Rare Pancreatic Tumor. Case Rep Oncol Med. 2016; https://doi.org/10.1155/2016/7523742.
Milojević BZ, Marković RM, Cvetković AM. Solid and cystic pseudopapillary tumor of the pancreas: a case report. Srp Arh Celok Lek. 2013;141(5-6):384–6.
Singh A, Mohan G, Chaturvedi S, Sarangi L. Solid pseudopapillary tumor of the pancreas: a lesser known entitiy-diagnosis and pitfalls: a case report. J Cytol. 2016;33(4):229–32.
Vassos N, Agaimy A, Klein P, Hohenberger W, Croner RS. Solid-pseudopapillary neoplasm (SPN) pancreas: case series and literature review on an enigmatic entity. Int J Clin Exp Pathol. 2013;6(6):1051–9.
Lakhtakia R, Al-Wahaibi K, Zahid KF, Malik KA, Burney IA. Solid pseudopapillary neoplasm of the pancreas: a case report with review of the diagnostic dilemmas and tumor behavior. Oman Med J. 2013;28(6):441–4.
Springer S, Wang Y, Dal Molin M. A combination of molecular markers and clinical features improve the classification of pancreatic cysts. Gastroenterology. 2015;149(6):1501–10.
Author information
Authors and Affiliations
Corresponding author
Ethics declarations
Conflict of interest
M. Portelli, S. Bozanic, D. Pisani, K. Cortis and J.-E. Abela declare that they have no competing interests.
Ethical standards
This article does not contain any studies with human participants or animals performed by any of the authors. Informed consent was obtained from all individual participants included in this case series. Copies of the consent forms are available for review from the Editor-in-Chief of this journal upon request.
Rights and permissions
About this article
Cite this article
Portelli, M., Bozanic, S., Pisani, D. et al. Pseudopapillary tumours of the pancreas. Eur Surg 50, 189–194 (2018). https://doi.org/10.1007/s10353-018-0520-6
Received:
Accepted:
Published:
Issue Date:
DOI: https://doi.org/10.1007/s10353-018-0520-6