Histiocyte-rich rhabdomyoblastic tumor is a recently described skeletal muscle neoplasm of uncertain malignant potential, characterized by slow growth, a fibrous capsule containing peripheral lymphoid aggregates, spindle-to-epithelioid cells with a rhabdomyoblastic immunophenotype, and a dense histiocytic infiltrate. It most commonly arises within the muscles of the lower legs and trunk in young-to-middle–aged men, and initial reports suggest indolent behavior. In this paper, we present two additional cases of histiocyte-rich rhabdomyoblastic tumor with similar clinicopathologic features and discuss the differential diagnosis including its overlap with inflammatory leiomyosarcoma.
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The original version of this article was revised: The family name of the co-author of the article mentioned above was incorrectly spelled. The correct name should have been “Melanie Bourgeau” instead of “Melanine Bourgeau”. The has been corrected.
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Bourgeau, M., Martinez, A.P. Histiocyte-rich rhabdomyoblastic tumor: a report of two cases and a review of the differential diagnoses. Virchows Arch (2020). https://doi.org/10.1007/s00428-020-02857-x
- Histiocyte-rich rhabdomyoblastic tumor
- Inflammatory leiomyosarcoma
- Smooth muscle tumors