Abstract
The components of the hepatic vascular system (hepatic arteries, portal and hepatic veins, sinusoids, and lymphatics) can be damaged by various types of injury. Each of the resulting conditions is rare, which has limited knowledge and awareness. In the last two decades, international collaborations have allowed to reach critical masses of data, which has driven significant progresses in understanding and management of vascular disorders of the liver. The present paper discusses definitions, denominations, and diagnosis of such vascular disorders with the exception of those affecting hepatic arteries. Evolving pathogenic or pathophysiologic views relevant to the clinical aspects are also overviewed.
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This editorial is part of the Topical Collection on Vascular liver lesions: contemporary views on long-recognized entities
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Valla, DC., Cazals-Hatem, D. Vascular liver diseases on the clinical side: definitions and diagnosis, new concepts. Virchows Arch 473, 3–13 (2018). https://doi.org/10.1007/s00428-018-2331-3
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DOI: https://doi.org/10.1007/s00428-018-2331-3
Keywords
- Budd-Chiari syndrome
- Hepatic vein thrombosis
- Portal vein thrombosis
- Portal cavernoma
- Idiopathic portal hypertension
- Idiopathic noncirrhotic intrahepatic portal hypertension
- Obliterative portal venopathy
- Nodular regenerative hyperplasia
- Incomplete septal cirrhosis
- Hepatoportal sclerosis
- Sinusoidal obstruction syndrome
- Venoocclusive disease
- Nonobstructive sinusoidal dilatation
- Peliosis
- Congenital portosystemic shunt
- Abernethy malformation