Amniotic band syndrome associated with limited dorsal myeloschisis: a case report of an unusual case and review of the literature


Amniotic band syndrome (ABS) has been known since ancient times. Descriptions in modern medicine have occurred since the mid-nineteenth century. The association of the amniotic band syndrome with tethered cord is rare. It was generally thought to be incompatible with life. Of late, with better imaging, there have been case reports of amniotic bands causing cord tethering in neurosurgical literature, but its association with limited dorsal myeloschisis has hitherto not been described. We report a case of amniotic band syndrome (ABS) associated with a cervical limited dorsal myeloschisis (LDM) in a child of 2 and a half years old. The management of LDM in ABS is essentially the same as in isolated cases

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Chatterjee, S., Rao, K.S.M. & Nadkarni, A. Amniotic band syndrome associated with limited dorsal myeloschisis: a case report of an unusual case and review of the literature. Childs Nerv Syst (2020).

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  • Amniotic band syndrome/sequence
  • ABS
  • Limited dorsal myeloschisis
  • LDM
  • Tethered cord syndrome