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Chronic catastrophic-like antiphospholipid syndrome: a “smoldering” variant?

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Abstract

Catastrophic antiphospholipid syndrome (CAPS) is characterized by life-threatening diffuse thrombotic manifestations involving particularly small vessels of kidney, lungs, brain and skin. We report a 20-year-old female with systemic lupus erythematosus and secondary antiphospholipid syndrome who presented typical organ and histological involvement as seen in CAPS but with protracted course suggesting a “smoldering” form of the disease.

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Acknowledgments

M. S. is currently receiving a scholarship from Conselho Nacional de Desenvolvimento Científico e Tecnológico (CNPq).

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Authors and Affiliations

  1. Universidade Federal da Bahia (UFBA), Salvador, Brazil

    Daniel Athanazio

  2. Clínica BIOS, Salvador, Brazil

    Maria Cristina Rocha

  3. Hospital Aliança, Salvador, Brazil

    Túlio Geraldo de Souza e Souza & Sérgio Jezler

  4. Escola Bahiana de Medicina e Saúde Pública (EBMSP), Salvador, Brazil

    Natália Oliveira e Silva & Mittermayer Barreto Santiago

  5. Rheumatology Service, Hospital Santa Izabel, Salvador, Brazil

    Mittermayer Barreto Santiago

  6. Praça Conselheiro Almeida Couto, 500, Nazaré, Salvador, Bahia, CEP 40000-000, Brazil

    Mittermayer Barreto Santiago

Authors
  1. Daniel Athanazio
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  2. Maria Cristina Rocha
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  3. Túlio Geraldo de Souza e Souza
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  4. Natália Oliveira e Silva
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  5. Sérgio Jezler
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  6. Mittermayer Barreto Santiago
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Correspondence to Mittermayer Barreto Santiago.

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Athanazio, D., Rocha, M.C., de Souza e Souza, T.G. et al. Chronic catastrophic-like antiphospholipid syndrome: a “smoldering” variant?. Rheumatol Int 30, 123–125 (2009). https://doi.org/10.1007/s00296-009-0913-8

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  • DOI: https://doi.org/10.1007/s00296-009-0913-8

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