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Hepatic nodular hyperplasia in a boy with Alagille syndrome: CT and MR appearances

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Abstract

A boy with Alagille syndrome complicated by hepatic nodular hyperplasia (HNH) is reported. During pre-transplantation evaluation, CT and MRI revealed a large hepatic lesion with multiple small nodular lesions. Angiography demonstrated a large hypervascular lesion and CT arterial portography (CTAP) showed a portal perfusion defect corresponding to the lesion. CTAP also revealed large portal vein branches running through the lesion. Although hepatocellular carcinoma is known to accompany Alagille syndrome, HNH should also be considered when large vessels running through the lesion are demonstrated.

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Authors and Affiliations

  1. Department of Radiology, Faculty of Medicine, Kyushu University, Japan, , , , , , JP

    Tsuyoshi Tajima, Hiroshi Honda, Toshirou Kuroiwa, Kengo Yoshimitsu, Hiroyuki Irie, Yasuo Kuwabara & Kouji Masuda

  2. Department of Surgery II, Faculty of Medicine, Kyushu University, Japan, , , , , , JP

    Katsuhiko Yanaga

  3. Department of Pathology II, Faculty of Medicine, Kyushu University, Japan, , , , , , JP

    Kenichi Taguchi

Authors
  1. Tsuyoshi Tajima
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  2. Hiroshi Honda
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  3. Katsuhiko Yanaga
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  4. Toshirou Kuroiwa
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  5. Kengo Yoshimitsu
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  6. Hiroyuki Irie
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  7. Yasuo Kuwabara
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  8. Kenichi Taguchi
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  9. Kouji Masuda
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Additional information

Received: 7 March 2000 Revised: 3 October 2000 Accepted: 5 March 2001

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Tajima, T., Honda, H., Yanaga, K. et al. Hepatic nodular hyperplasia in a boy with Alagille syndrome: CT and MR appearances. Pediatric Radiology 31, 584–588 (2001). https://doi.org/10.1007/s002470100510

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  • DOI: https://doi.org/10.1007/s002470100510

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