Abstract
Two different forms of dyssegmental dysplasia, mild and severe, can be distinguished on clinical, radiographic and chondro-osseous morphologic grounds. The milder Rolland-Desbuquois type is frequently characterised by survival beyond the newborn period. The lethal Silverman-Handmaker type has distinctive and more severe findings. In this paper, a rare case of the Rolland-Desbuquois type is presented. The case is unusual because although it was the milder form, the child died on the 10th day of life.
Similar content being viewed by others
Author information
Authors and Affiliations
Additional information
Received: 15 January 1997 Accepted: 21 March 1997
Rights and permissions
About this article
Cite this article
d'Orey, M., Mateus, M., Guimara˜es, H. et al. Dyssegmental dysplasia: a case report of a Rolland-Desbuquois type. Pediatric Radiology 27, 948–950 (1997). https://doi.org/10.1007/s002470050279
Issue Date:
DOI: https://doi.org/10.1007/s002470050279